Taquicardia ortostática postural em adolescentes: como e por que diagnosticar

Postural Orthostatic Tachycardia Syndrome (POTS) is a rare heterogeneous syndrome secondary to a disorder of the autonomic nervous system, characterized by sustained symptomatic sinus tachycardia in the upright position without arterial hypotension. Chronic symptoms are nonspecific and involve multi...

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Main Authors: Camila Magalhães Silva, Ludimila Dos Anjos Teixeira Romão, Lalleinny Franthiesca da Costa Alves, Roberta Leão Bassi, Rose Mary Ferreira Lisboa da Silva, Fátima Derlene da Rocha Araújo, Zilda Maria Alves Meira
Format: Article
Language:English
Published: Sociedade Brasileira de Pediatria 2024-12-01
Series:Residência Pediátrica
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Online Access:https://cdn.publisher.gn1.link/residenciapediatrica.com.br/pdf/v14n4a1161.pdf
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author Camila Magalhães Silva
Ludimila Dos Anjos Teixeira Romão
Lalleinny Franthiesca da Costa Alves
Roberta Leão Bassi
Rose Mary Ferreira Lisboa da Silva
Fátima Derlene da Rocha Araújo
Zilda Maria Alves Meira
author_facet Camila Magalhães Silva
Ludimila Dos Anjos Teixeira Romão
Lalleinny Franthiesca da Costa Alves
Roberta Leão Bassi
Rose Mary Ferreira Lisboa da Silva
Fátima Derlene da Rocha Araújo
Zilda Maria Alves Meira
author_sort Camila Magalhães Silva
collection DOAJ
description Postural Orthostatic Tachycardia Syndrome (POTS) is a rare heterogeneous syndrome secondary to a disorder of the autonomic nervous system, characterized by sustained symptomatic sinus tachycardia in the upright position without arterial hypotension. Chronic symptoms are nonspecific and involve multiple organ systems, often leading to debilitating effects on the individuals quality of life. Although relatively unfamiliar to cardiologists, it is an essential entity in the differential diagnosis of pre-syncope. We present a case report of an adolescent referred to pediatric cardiology to investigate intermittent and recurrent episodes of sweating, chest pain, muscle weakness without loss of consciousness, palpitations, pallor, and tachycardia. During the medical history, she also reported other symptoms impacting her daily activities and school performance. Following a comprehensive physical examination (including heart rate and blood pressure assessment) and additional tests (electrocardiogram, transthoracic echocardiogram, and Tilt Test), she was diagnosed with POTS. Subsequently, a treatment plan, both pharmacological and non-pharmacological, was initiated, resulting in an improvement in her quality of life and symptom control. Recognition of this recently described medical condition depends on clinical suspicion during the medical history and physical examination, allowing for the implementation of treatment with the aim of enhancing the patients quality of life.
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publisher Sociedade Brasileira de Pediatria
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spelling doaj-art-f625d30400854f3ab2594b8569a495ae2025-01-06T19:34:32ZengSociedade Brasileira de PediatriaResidência Pediátrica2236-68142024-12-0114410.25060/residpediatr-2024.v14n4-1161Taquicardia ortostática postural em adolescentes: como e por que diagnosticarCamila Magalhães Silva0Ludimila Dos Anjos Teixeira Romão1Lalleinny Franthiesca da Costa Alves2Roberta Leão Bassi3Rose Mary Ferreira Lisboa da Silva4Fátima Derlene da Rocha Araújo5Zilda Maria Alves Meira6Hospital das Clínicas da Universidade Federal de Minas Gerais, Cardiologia Pediátrica - Belo Horizonte - Minas Gerais - BrasilHospital das Clínicas da Universidade Federal de Minas Gerais, Cardiologia Pediátrica - Belo Horizonte - Minas Gerais - BrasilHospital das Clínicas da Universidade Federal de Minas Gerais, Cardiologia Pediátrica - Belo Horizonte - Minas Gerais - BrasilHospital das Clínicas da Universidade Federal de Minas Gerais, Cardiologia Pediátrica - Belo Horizonte - Minas Gerais - BrasilUniversidade Federal de Minas Gerais, Cardiologia - Belo Horizonte - Minas Gerais - Brasil.Hospital das Clínicas da Universidade Federal de Minas Gerais, Cardiologia Pediátrica - Belo Horizonte - Minas Gerais - BrasilHospital das Clínicas da Universidade Federal de Minas Gerais, Cardiologia Pediátrica - Belo Horizonte - Minas Gerais - BrasilPostural Orthostatic Tachycardia Syndrome (POTS) is a rare heterogeneous syndrome secondary to a disorder of the autonomic nervous system, characterized by sustained symptomatic sinus tachycardia in the upright position without arterial hypotension. Chronic symptoms are nonspecific and involve multiple organ systems, often leading to debilitating effects on the individuals quality of life. Although relatively unfamiliar to cardiologists, it is an essential entity in the differential diagnosis of pre-syncope. We present a case report of an adolescent referred to pediatric cardiology to investigate intermittent and recurrent episodes of sweating, chest pain, muscle weakness without loss of consciousness, palpitations, pallor, and tachycardia. During the medical history, she also reported other symptoms impacting her daily activities and school performance. Following a comprehensive physical examination (including heart rate and blood pressure assessment) and additional tests (electrocardiogram, transthoracic echocardiogram, and Tilt Test), she was diagnosed with POTS. Subsequently, a treatment plan, both pharmacological and non-pharmacological, was initiated, resulting in an improvement in her quality of life and symptom control. Recognition of this recently described medical condition depends on clinical suspicion during the medical history and physical examination, allowing for the implementation of treatment with the aim of enhancing the patients quality of life.https://cdn.publisher.gn1.link/residenciapediatrica.com.br/pdf/v14n4a1161.pdfgastritisesomeprazoleeosinophilic esophagitiscase reportseosinophils
spellingShingle Camila Magalhães Silva
Ludimila Dos Anjos Teixeira Romão
Lalleinny Franthiesca da Costa Alves
Roberta Leão Bassi
Rose Mary Ferreira Lisboa da Silva
Fátima Derlene da Rocha Araújo
Zilda Maria Alves Meira
Taquicardia ortostática postural em adolescentes: como e por que diagnosticar
Residência Pediátrica
gastritis
esomeprazole
eosinophilic esophagitis
case reports
eosinophils
title Taquicardia ortostática postural em adolescentes: como e por que diagnosticar
title_full Taquicardia ortostática postural em adolescentes: como e por que diagnosticar
title_fullStr Taquicardia ortostática postural em adolescentes: como e por que diagnosticar
title_full_unstemmed Taquicardia ortostática postural em adolescentes: como e por que diagnosticar
title_short Taquicardia ortostática postural em adolescentes: como e por que diagnosticar
title_sort taquicardia ortostatica postural em adolescentes como e por que diagnosticar
topic gastritis
esomeprazole
eosinophilic esophagitis
case reports
eosinophils
url https://cdn.publisher.gn1.link/residenciapediatrica.com.br/pdf/v14n4a1161.pdf
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