A low-fat amino acid diet reverses intestinal failure and shows good growth trends in five infants with diacylglycerol transferase 1 (DGAT1) deficiency: a prospective cohort study

A low-fat amino acid diet reverses intestinal failure and shows good growth trends in five infants with diacylglycerol transferase 1 (DGAT1) deficiency: a prospective cohort study

Abstract Background Congenital diarrheas and enteropathies (CODEs) caused by diacylglycerol transferase 1 (DGAT1) mutations often cause disease within 2 weeks after birth. If not treated properly, the disease can be life-threatening; therefore, early diagnosis and rational treatment strategies are e...

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Bibliographic Details
Main Authors:	Yuanyuan Zheng, Yongzhen Li, Cuifang Zheng, Lin Yang, Chongfan Zhang, Ying Huang, Yuhuan Wang, Tian Qian
Format:	Article
Language:	English
Published:	BMC 2024-11-01
Series:	Lipids in Health and Disease
Subjects:	Congenital diarrhea Diacylglycerol transferase 1 (DGAT1) mutation Growth retardation Low-fat amino acid diet Prospective cohort study
Online Access:	https://doi.org/10.1186/s12944-024-02348-x
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