Clinical and genetic features of UNC13D deficiency with hypogammaglobulinemia

BackgroundUNC13D deficiency is the most common form of familial hemophagocytic lymphohistiocytosis (FHL) in Asia. Hypogammaglobulinemia is a rare phenotype observed in both patients with FHL3 and sporadic hemophagocytic lymphohistiocytosis (HLH). Our observations suggest that UNC13D deficiency with...

Full description

Saved in:
Bibliographic Details
Main Authors: Linyan Xiong, Qin Zhao, Qian Zhao, Zhiyong Zhang, Yunfei An, Xuemei Tang, Hirokazu Kanegane, Xi Yang, Xiaodong Zhao
Format: Article
Language:English
Published: Frontiers Media S.A. 2025-08-01
Series:Frontiers in Immunology
Subjects:
Online Access:https://www.frontiersin.org/articles/10.3389/fimmu.2025.1628507/full
Tags: Add Tag
No Tags, Be the first to tag this record!