One case of C1q nephropathy

<正>C1q肾病(C1qN)是一种罕见的肾小球疾病,多见于儿童和青少年。临床表现多样,可以出现肾病综合征、伴有或不伴有血尿的轻度蛋白尿、复发性肉眼血尿、急性肾损伤和快速进展性肾小球肾炎等,其中以肾病综合征最为常见。C1qN诊断主要依赖于免疫荧光显示肾小球系膜区C1q为主沉积且排除其他可引起C1q沉积的免疫介导疾病,肾脏病理学常见3种类型即微小病变性肾病(MCD)、局灶节段性肾小球硬化(FSGS)以及系膜增生性肾小球肾炎(MsPGN)<sup>[1]</sup>。现...

Full description

Saved in:
Bibliographic Details
Main Authors: CHU Rui, DING Hong, WANG Sha-xi, WANG Rui, MAO Mei-qi, LIU Xiao-tong, MEI Yu-ming
Format: Article
Language:zho
Published: Editorial Department of Journal of Clinical Nephrology 2019-01-01
Series:Linchuang shenzangbing zazhi
Subjects:
Online Access:http://www.lcszb.com/thesisDetails?columnId=57910233&Fpath=home&index=0
Tags: Add Tag
No Tags, Be the first to tag this record!