The Biomechanics of Fibrillin Microfibrils: Lessons from the Ciliary Zonule

Marfan syndrome is an inherited connective tissue disorder that affects the cardiovascular, musculoskeletal, and ocular systems. It is caused by pathogenic variants in the fibrillin-1 gene (<i>FBN1</i>). Fibrillin is a primary component of microfibrils, which are found throughout the ext...

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Bibliographic Details
Main Authors: Pooja Rathaur, Juan Rodriguez, John Kuchtey, Samuel Insignares, Wendell B. Jones, Rachel W. Kuchtey, Steven Bassnett
Format: Article
Language:English
Published: MDPI AG 2024-12-01
Series:Cells
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Online Access:https://www.mdpi.com/2073-4409/13/24/2097
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