Acute Bilateral Retrobulbar Optic Neuritis Revealing Sphenoethmoidal Sinus Neuroendocrine Carcinoma

Primary sinonasal neuroendocrine carcinoma is a rare tumor of extreme malignancy. The diagnosis is often made at an advanced stage. The most recently documented treatment for nonmetastatic paranasal sinus neuroendocrine carcinoma consists of chemotherapy (cisplatin-VP16) followed by radiotherapy. Su...

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Bibliographic Details
Main Authors: Belfaiza Soukaina, Marion Chatain, Benjelloul Fatiha
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2023-01-01
Series:Indian Journal of Medical Specialities
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Online Access:https://journals.lww.com/10.4103/injms.injms_130_22
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Summary:Primary sinonasal neuroendocrine carcinoma is a rare tumor of extreme malignancy. The diagnosis is often made at an advanced stage. The most recently documented treatment for nonmetastatic paranasal sinus neuroendocrine carcinoma consists of chemotherapy (cisplatin-VP16) followed by radiotherapy. Surgery is reserved for resectable tumors that do not respond well to chemotherapy. We report the case of a patient admitted for acute bilateral Retrobulbular optic neuropathy (RBON) revealing a sphenoethmoidal sinus neuroendocrine carcinoma.
ISSN:0976-2884
0976-2892