Sanjad-Sakati Syndrome Dental Management: A Case Report

Sanjad-Sakati syndrome (SSS) is a rare genetic disorder with autosomal recessive pattern of inheritance characterized by hypoparathyroidism, sever growth failure, mental retardation, susceptibility to chest infection, and dentofacial anomalies. A child with SSS was referred to the dental departments...

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Main Author: Hisham Y. El Batawi
Format: Article
Language:English
Published: Wiley 2013-01-01
Series:Case Reports in Dentistry
Online Access:http://dx.doi.org/10.1155/2013/184084
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author Hisham Y. El Batawi
author_facet Hisham Y. El Batawi
author_sort Hisham Y. El Batawi
collection DOAJ
description Sanjad-Sakati syndrome (SSS) is a rare genetic disorder with autosomal recessive pattern of inheritance characterized by hypoparathyroidism, sever growth failure, mental retardation, susceptibility to chest infection, and dentofacial anomalies. A child with SSS was referred to the dental departmentseeking dental help for sever dental caries which was attributed to his dietary habits and quality of dental tissues. Full restorative rehabilitation was done under general anesthesia. Two years later, the child presented with recurrent caries affecting uncrowned teeth. High carries recurrence rate was blamed for the nutritional habits endorsed by the parents. Only steel crowned teeth survived such hostile oral environment which suggested shifting of treatment strategy towards full coverage restorations instead of classical cavity preparations and fillings during a second attempt for dental treatment under general anesthesia and for the dental treatment of two cousins of the same child. The author recommends effective health education for parents including the nature of their child’s genetic disorder, nutritional needs, and dental health education to improve the life style of such children.
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spelling doaj-art-3d9095748edb45f5b7d2a7fc7b8bf6b32025-02-03T05:47:26ZengWileyCase Reports in Dentistry2090-64472090-64552013-01-01201310.1155/2013/184084184084Sanjad-Sakati Syndrome Dental Management: A Case ReportHisham Y. El Batawi0Pediatric Dentistry, Sharjah University City, P.O. Box 27272, Sharjah, UAESanjad-Sakati syndrome (SSS) is a rare genetic disorder with autosomal recessive pattern of inheritance characterized by hypoparathyroidism, sever growth failure, mental retardation, susceptibility to chest infection, and dentofacial anomalies. A child with SSS was referred to the dental departmentseeking dental help for sever dental caries which was attributed to his dietary habits and quality of dental tissues. Full restorative rehabilitation was done under general anesthesia. Two years later, the child presented with recurrent caries affecting uncrowned teeth. High carries recurrence rate was blamed for the nutritional habits endorsed by the parents. Only steel crowned teeth survived such hostile oral environment which suggested shifting of treatment strategy towards full coverage restorations instead of classical cavity preparations and fillings during a second attempt for dental treatment under general anesthesia and for the dental treatment of two cousins of the same child. The author recommends effective health education for parents including the nature of their child’s genetic disorder, nutritional needs, and dental health education to improve the life style of such children.http://dx.doi.org/10.1155/2013/184084
spellingShingle Hisham Y. El Batawi
Sanjad-Sakati Syndrome Dental Management: A Case Report
Case Reports in Dentistry
title Sanjad-Sakati Syndrome Dental Management: A Case Report
title_full Sanjad-Sakati Syndrome Dental Management: A Case Report
title_fullStr Sanjad-Sakati Syndrome Dental Management: A Case Report
title_full_unstemmed Sanjad-Sakati Syndrome Dental Management: A Case Report
title_short Sanjad-Sakati Syndrome Dental Management: A Case Report
title_sort sanjad sakati syndrome dental management a case report
url http://dx.doi.org/10.1155/2013/184084
work_keys_str_mv AT hishamyelbatawi sanjadsakatisyndromedentalmanagementacasereport