Surgical Management of Desmoid Tumors—Patient Selection, Timing, and Approach

Desmoid tumors are rare, deep-seated myofibroblastic tumors with an unpredictable course, ranging from spontaneous regression to infiltrative growth and locally aggressive behavior, but without metastatic potential. Over the past few decades, advances in understanding their natural history, underlyi...

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Main Authors: Catherine Sarre Lazcano, Alessandro Gronchi
Format: Article
Language:English
Published: MDPI AG 2025-07-01
Series:Current Oncology
Subjects:
Online Access:https://www.mdpi.com/1718-7729/32/7/408
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author Catherine Sarre Lazcano
Alessandro Gronchi
author_facet Catherine Sarre Lazcano
Alessandro Gronchi
author_sort Catherine Sarre Lazcano
collection DOAJ
description Desmoid tumors are rare, deep-seated myofibroblastic tumors with an unpredictable course, ranging from spontaneous regression to infiltrative growth and locally aggressive behavior, but without metastatic potential. Over the past few decades, advances in understanding their natural history, underlying molecular pathways, and patient care priorities have shifted the treatment paradigm from upfront surgical resection to initial active surveillance, with further treatment dictated by continuous disease progression or associated symptoms. However, there are still specific scenarios where surgery continues to play an important role in locoregional treatment and symptom control. This article will focus on current treatment strategies and surgical indications in adult patients with desmoid tumors, emphasizing patient selection, anatomic site-specific considerations, and surgical technique. Understanding the nuanced role of surgery within the growing treatment landscape is key for individualized patient care in a multidisciplinary setting to optimize quality of life and long-term outcomes.
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series Current Oncology
spelling doaj-art-2ad5287f7a694cbb937cbb1e80e0c4692025-08-20T03:58:31ZengMDPI AGCurrent Oncology1198-00521718-77292025-07-0132740810.3390/curroncol32070408Surgical Management of Desmoid Tumors—Patient Selection, Timing, and ApproachCatherine Sarre Lazcano0Alessandro Gronchi1Division of Surgical Oncology, Department of Surgery, University of Toronto, Toronto, ON M5S 1A1, CanadaSarcoma Service, Department of Surgery, Fondazione IRCCS Istituto Nazionale dei Tumori, 20133 Milan, ItalyDesmoid tumors are rare, deep-seated myofibroblastic tumors with an unpredictable course, ranging from spontaneous regression to infiltrative growth and locally aggressive behavior, but without metastatic potential. Over the past few decades, advances in understanding their natural history, underlying molecular pathways, and patient care priorities have shifted the treatment paradigm from upfront surgical resection to initial active surveillance, with further treatment dictated by continuous disease progression or associated symptoms. However, there are still specific scenarios where surgery continues to play an important role in locoregional treatment and symptom control. This article will focus on current treatment strategies and surgical indications in adult patients with desmoid tumors, emphasizing patient selection, anatomic site-specific considerations, and surgical technique. Understanding the nuanced role of surgery within the growing treatment landscape is key for individualized patient care in a multidisciplinary setting to optimize quality of life and long-term outcomes.https://www.mdpi.com/1718-7729/32/7/408desmoid tumoraggressive fibromatosissurgerymarginsfunctional outcomes
spellingShingle Catherine Sarre Lazcano
Alessandro Gronchi
Surgical Management of Desmoid Tumors—Patient Selection, Timing, and Approach
Current Oncology
desmoid tumor
aggressive fibromatosis
surgery
margins
functional outcomes
title Surgical Management of Desmoid Tumors—Patient Selection, Timing, and Approach
title_full Surgical Management of Desmoid Tumors—Patient Selection, Timing, and Approach
title_fullStr Surgical Management of Desmoid Tumors—Patient Selection, Timing, and Approach
title_full_unstemmed Surgical Management of Desmoid Tumors—Patient Selection, Timing, and Approach
title_short Surgical Management of Desmoid Tumors—Patient Selection, Timing, and Approach
title_sort surgical management of desmoid tumors patient selection timing and approach
topic desmoid tumor
aggressive fibromatosis
surgery
margins
functional outcomes
url https://www.mdpi.com/1718-7729/32/7/408
work_keys_str_mv AT catherinesarrelazcano surgicalmanagementofdesmoidtumorspatientselectiontimingandapproach
AT alessandrogronchi surgicalmanagementofdesmoidtumorspatientselectiontimingandapproach