Beta-talasemi major komplikasyonu olarak gelişen diabetes mellitus ve hipoparatiroidi
Beta-talasemi major ilk defa Cooley ve Lee tarafından tanımlanmış olup, β-globin zincir sentezinde azalma ile giden, resesif karakterli bir hemoglobin bozukluğudur. Homozigot olgular düzenli kan transfüzyonu gerektiren ağır anemi ile seyreder. Şelasyon ve transfüz- yon tedavisi kombinasyonu yaşam b...
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Main Authors: | Ayşe Özlem Kılıçaslan, Mustafa Kulaksızoğlu, Ruhuşen Kutlu |
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Format: | Article |
Language: | English |
Published: |
Selcuk University Press
2014-01-01
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Series: | Genel Tıp Dergisi |
Subjects: | |
Online Access: | https://dergipark.org.tr/tr/download/article-file/2156738 |
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