An updated overview of Juvenile systemic sclerosis in a French cohort

An updated overview of Juvenile systemic sclerosis in a French cohort

Abstract Background Systemic sclerosis encompasses a range of disorders characterized by vascular and connective tissue abnormalities. Although rare in pediatrics, juvenile systemic sclerosis (jSSc) is a severe and life-threatening condition that significantly impacts children’s development. This st...

Full description

Saved in:

Bibliographic Details
Main Authors:	Léa Jacquel, Rouba Bechara, Joëlle Terzic, Anne-Cécile Rameau, Emmanuel Chatelus, Linda Rossi-Semerano, Isabelle Kone-Paut, Ulrich Meinzer, Irène Lemelle, Charlotte Rebelle, Diego Urbina, Pascal Pillet, Pauline Choquet, Jad El Maamari, Ariane Zaloszyc, SOFREMIP
Format:	Article
Language:	English
Published:	BMC 2025-02-01
Series:	Pediatric Rheumatology Online Journal
Subjects:	Scleroderma Systemic Juvenile systemic sclerosis Autoimmune disease Biological therapy
Online Access:	https://doi.org/10.1186/s12969-024-01043-6
Tags:	Add Tag No Tags, Be the first to tag this record!

Similar Items

Efficacy of divozilimab in the treatment of systemic sclerosis: results of the randomized phase III clinical trial BCD-132-5/LIBERIUS
by: L. P. Ananyeva, et al.
Published: (2025-02-01)

The efficacy and safety of divozilimab in patient with systemic sclerosis: 48-week results of the randomized double-blind placebo-controlled phase III clinical study LIBERIUS
by: L. P. Ananyeva, et al.
Published: (2025-05-01)

Developing consensus outcome measures in juvenile systemic sclerosis: a global survey of pediatric rheumatologists and literature review
by: Natalia Vasquez-Canizares, et al.
Published: (2025-05-01)

Epidemiology of systemic sclerosis in the Asia-Pacific region: a systematic review and meta-analysis
by: Ajanee Mahakkanukrauh, et al.
Published: (2025-12-01)

Effect of rituximab on heart involvement in systemic sclerosis
by: L. A. Garzanova, et al.
Published: (2019-01-01)

The problem of activity in systemic scleroderma
by: N G Guseva, et al.
Published: (2013-06-01)

EPIDEMIOLOGICAL PROFILE OF PATIENTS WITH SYSTEMIC SCLEROSIS TREATED AT A QUATERNARY HOSPITAL IN THE STATE OF SÃO PAULO
by: Pedro Henrique de Magalhães Tenório, et al.
Published: (2025-06-01)

EFFECT OF AT ORVASTATIN ON THE TIME COURSE OF CHANGESIN INFLAMMATORY MARKERS IN SYSTEMIC SCLERODERMA
by: R T Alekperov, et al.
Published: (2011-04-01)

Evaluation of the Efficiency of Treatment with Rituximab for Systemic Scleroderma (A Case Report)
by: E. N. Harlamova, et al.
Published: (2021-01-01)

Renal function during long-term therapy with rituximab in patients with systemic sclerosis
by: M. N. Starovoitova, et al.
Published: (2023-10-01)

Symptoms of Oesophageal Affection in Children With Scleroderma According to Mano-Impedancemetry: A Case Series
by: Marina Ju. Stepanyan, et al.
Published: (2019-02-01)

Experience with Lipofilling in Children with Localized Scleroderma: Case Study
by: Alina R. Misbakhova, et al.
Published: (2024-11-01)

Clinical and Epidemiological Characteristics of Scleroderma in Children of the Samara Region: a Single-Stage Retrospective Study
by: Juliya S. Bogomolova, et al.
Published: (2025-05-01)

The state of the oral microflora in patients with systemic sclerosis
by: M. S. Yesayan, et al.
Published: (2021-10-01)

The impact of altered hands function on working ability of patients with systemic sclerosis
by: Vidaković Predrag, et al.
Published: (2020-01-01)

Dialyse péritonéale chez l'enfant : Approches physiopathologiques, prescription et gestion des complications pour un traitement adéquat.
by: RoubaA Bechara, et al.
Published: (2025-06-01)

UNILATERAL LUNG INJURY IN SCLERODERMA SYSTEMATICA: A CASE REPORT
by: R. T. Alekperov, et al.
Published: (2014-09-01)

Combination of subtotal pneumofibrosis and post-COVID pulmonary complications in the context of the progression of systemic sclerosis (clinical observation)
by: M. V. Mnikhovich, et al.
Published: (2024-12-01)

Challenges in diagnosis and treatment of scleroderma renal crisis (clinical case report)
by: E. M. Mishina, et al.
Published: (2025-06-01)

Avascular Necrosis of the Foot and Ankle in a Patient with Systemic Sclerosis: A Case Based Review
by: H. Wastyn, et al.
Published: (2021-02-01)

Scleroderma Renal Crisis as Initial Presentation of Scleroderma
by: Sahil Bagai, et al.
Published: (2022-04-01)

Short-term absolute B-cell counts monitoring in systemic sclerosis patients treated with rituximab
by: L. P. Ananieva, et al.
Published: (2020-09-01)

DIAGNOSTIC VALUE OF CERULOPLASMIN IN SYSTEMIC SCLERODERMA
by: O. I. Emelyanova, et al.
Published: (2019-05-01)

Intravenous iloprost in the combination therapy of vascular disorders in patients with systemic connective tissue diseases
by: Aleksandr Vitalyevich Volkov, et al.
Published: (2013-06-01)

Systemic sclerosis in Egyptian population with emphasis on clinical and nailfold capillaroscopic features
by: Amira Elsonbaty, et al.
Published: (2025-08-01)

Modern tactics of managing patients with pulmonary arterial hypertension associated with systemic connective tissue diseases.
by: O. O. Khaniukov, et al.
Published: (2018-06-01)

Morphea profunda – a case report of deep localized scleroderma with severe thorax deformity
by: Natalia Tekiela, et al.
Published: (2025-01-01)

Drug-induced fibrosing syndromes: A scoping review
by: Sakir Ahmed, et al.
Published: (2019-01-01)

Сatalase antibodies in patients with systemic scleroderma as a diagnostic and prognostic marker of the disease
by: O. I. Emelyanova, et al.
Published: (2021-01-01)

The significance of smoking as a risk factor for the disorder of the obstructive pulmonary pattern in the patients with systemic sclerosis
by: Stefanović-Nešković Jelena, et al.
Published: (2019-01-01)

Use of the international systemic scleroderma activity index
by: Maya Nikolayevna Starovoitova, et al.
Published: (2013-03-01)

Systemic Sclerosis – A Diagnostic Challenge or a Clinically Controllable Disease?
by: Olga Kądziołka, et al.
Published: (2025-06-01)

Is Still's Disease an Autoinflammatory Syndrome?
by: Linda Rossi-Semerano, et al.
Published: (2012-01-01)

Autoimmunity and Lymphoma: Splenic Marginal Zone Lymphoma with Scleroderma and Chronic Hepatitis C Virus infection.
by: Ricardo García-Muñoz
Published: (2014-08-01)

SCLERODERMA-LIKE MASK OF OSTEOPOIKILIA
by: R G Mukhina, et al.
Published: (2002-04-01)

Single Sitting Bilateral Dacryocystorhinostomy for Chronic Dacryocystitis in A Patient with Scleroderma and Bipolar Disorder
by: Tara Shruthi, et al.
Published: (2021-04-01)

Relationship of endothelial dysfunction and kidney functional state in patients with systemic sclerosis
by: A M Basova, et al.
Published: (2009-12-01)

CLINICAL EVALUATION OF THE MANIFESTATIONS OF INTERSTITIAL LUNG INJURYIN SYSTEMIC SCLERODERMA FROM HIGH-RESOLUTION COMPUTER T OMOGRAPHY DATA
by: L P Anan'eva, et al.
Published: (2011-04-01)

Experience of successful autologous hematopoietic stem cell transplantation in patients with an unfavorable prognosis of systemic scleroderma
by: V. I. Mazurov, et al.
Published: (2022-07-01)

University proceedings. Volga region. Medical sciences
by: O.G. Radaykina, et al.
Published: (2025-04-01)