Aggressive Clinical Deterioration of Recurrent Extramammary Paget’s Disease: A Case Report

Extramammary Paget’s Disease (EMPD) is a rare intraepithelial malignancy of apocrine bearing glands, which occur usually in the perianal region, vulva, scrotum, penis and ax-illa. Most of the disease are treated by surgical resection and th...

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Main Authors: Sewon Lee, Sang Yoon Kim, Heejin Bang, Kyoung Eun Lee
Format: Article
Language:English
Published: Ewha Womans University College of Medicine 2022-10-01
Series:The Ewha Medical Journal
Subjects:
Online Access:http://www.e-emj.org/archive/view_article?pid=emj-45-4-15
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author Sewon Lee
Sang Yoon Kim
Heejin Bang
Kyoung Eun Lee
author_facet Sewon Lee
Sang Yoon Kim
Heejin Bang
Kyoung Eun Lee
author_sort Sewon Lee
collection DOAJ
description Extramammary Paget’s Disease (EMPD) is a rare intraepithelial malignancy of apocrine bearing glands, which occur usually in the perianal region, vulva, scrotum, penis and ax-illa. Most of the disease are treated by surgical resection and the prognosis is generally good. Even though recurrent disease, it is usually slowly progressed with good prognosis. Here we describe the case of a 70-year-old male who has presented with initially just as an EMPD component of squamous cell carcinoma in inguinal skin, but he showed recur-rence of EMPD. The disease has progressed rapidly, finally he died of that EMPD in 2 months of recurrence. The purpose of this study is to report the rare case of fulminant disease course of EMPD after recurrence.
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institution Kabale University
issn 2234-2591
language English
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publisher Ewha Womans University College of Medicine
record_format Article
series The Ewha Medical Journal
spelling doaj-art-fff11e4d46dd483787466da92b04de6b2024-12-16T08:43:15ZengEwha Womans University College of MedicineThe Ewha Medical Journal2234-25912022-10-0145410.12771/emj.2022.e15emj-45-4-15Aggressive Clinical Deterioration of Recurrent Extramammary Paget’s Disease: A Case ReportSewon LeeSang Yoon KimHeejin BangKyoung Eun LeeExtramammary Paget’s Disease (EMPD) is a rare intraepithelial malignancy of apocrine bearing glands, which occur usually in the perianal region, vulva, scrotum, penis and ax-illa. Most of the disease are treated by surgical resection and the prognosis is generally good. Even though recurrent disease, it is usually slowly progressed with good prognosis. Here we describe the case of a 70-year-old male who has presented with initially just as an EMPD component of squamous cell carcinoma in inguinal skin, but he showed recur-rence of EMPD. The disease has progressed rapidly, finally he died of that EMPD in 2 months of recurrence. The purpose of this study is to report the rare case of fulminant disease course of EMPD after recurrence.http://www.e-emj.org/archive/view_article?pid=emj-45-4-15paget’s diseaseextramammaryaggressive extramammary paget’s disease
spellingShingle Sewon Lee
Sang Yoon Kim
Heejin Bang
Kyoung Eun Lee
Aggressive Clinical Deterioration of Recurrent Extramammary Paget’s Disease: A Case Report
The Ewha Medical Journal
paget’s disease
extramammary
aggressive extramammary paget’s disease
title Aggressive Clinical Deterioration of Recurrent Extramammary Paget’s Disease: A Case Report
title_full Aggressive Clinical Deterioration of Recurrent Extramammary Paget’s Disease: A Case Report
title_fullStr Aggressive Clinical Deterioration of Recurrent Extramammary Paget’s Disease: A Case Report
title_full_unstemmed Aggressive Clinical Deterioration of Recurrent Extramammary Paget’s Disease: A Case Report
title_short Aggressive Clinical Deterioration of Recurrent Extramammary Paget’s Disease: A Case Report
title_sort aggressive clinical deterioration of recurrent extramammary paget s disease a case report
topic paget’s disease
extramammary
aggressive extramammary paget’s disease
url http://www.e-emj.org/archive/view_article?pid=emj-45-4-15
work_keys_str_mv AT sewonlee aggressiveclinicaldeteriorationofrecurrentextramammarypagetsdiseaseacasereport
AT sangyoonkim aggressiveclinicaldeteriorationofrecurrentextramammarypagetsdiseaseacasereport
AT heejinbang aggressiveclinicaldeteriorationofrecurrentextramammarypagetsdiseaseacasereport
AT kyoungeunlee aggressiveclinicaldeteriorationofrecurrentextramammarypagetsdiseaseacasereport