Current state of cardiac troponin testing in Duchenne muscular dystrophy cardiomyopathy: review and recommendations from the Parent Project Muscular Dystrophy expert panel

Cardiac disease is now the leading cause of death in Duchenne muscular dystrophy (DMD). Clinical evaluations over time have demonstrated asymptomatic cardiac troponin elevations and acute elevations are associated with symptoms and cardiac dysfunction in DMD. Clinicians require a better understandin...

Full description

Saved in:
Bibliographic Details
Main Authors: Christopher F Spurney, Lawrence Charnas, Linda Cripe, Kan Hor, Nicholas King, Kathi Kinnett, Elizabeth M McNally, John-Michael Sauer, Lee Sweeney, Chet Villa, Larry W Markham
Format: Article
Language:English
Published: BMJ Publishing Group 2021-02-01
Series:Open Heart
Online Access:https://openheart.bmj.com/content/8/1/e001592.full
Tags: Add Tag
No Tags, Be the first to tag this record!
_version_ 1846170350291779584
author Christopher F Spurney
Lawrence Charnas
Linda Cripe
Kan Hor
Nicholas King
Kathi Kinnett
Elizabeth M McNally
John-Michael Sauer
Lee Sweeney
Chet Villa
Larry W Markham
author_facet Christopher F Spurney
Lawrence Charnas
Linda Cripe
Kan Hor
Nicholas King
Kathi Kinnett
Elizabeth M McNally
John-Michael Sauer
Lee Sweeney
Chet Villa
Larry W Markham
author_sort Christopher F Spurney
collection DOAJ
description Cardiac disease is now the leading cause of death in Duchenne muscular dystrophy (DMD). Clinical evaluations over time have demonstrated asymptomatic cardiac troponin elevations and acute elevations are associated with symptoms and cardiac dysfunction in DMD. Clinicians require a better understanding of the relationship of symptoms, troponin levels and progression of cardiac disease in DMD. As clinical trials begin to assess novel cardiac therapeutics in DMD, troponin levels in DMD are important for safety monitoring and outcome measures. The Parent Project Muscular Dystrophy convened an expert panel of cardiologists, scientists, and regulatory and industry specialists on 16 December 2019 in Silver Spring, Maryland and reviewed published and unpublished data from their institutions. The panel recommended retrospective troponin data analyses, prospective longitudinal troponin collection using high-sensitivity cardiac troponin I assays, inclusion of troponin in future clinical trial outcomes and future development of clinical guidelines for monitoring and treating troponin elevations in DMD.
format Article
id doaj-art-fe6ebdacbf0c47549115ec21cf90fdee
institution Kabale University
issn 2053-3624
language English
publishDate 2021-02-01
publisher BMJ Publishing Group
record_format Article
series Open Heart
spelling doaj-art-fe6ebdacbf0c47549115ec21cf90fdee2024-11-12T02:50:09ZengBMJ Publishing GroupOpen Heart2053-36242021-02-018110.1136/openhrt-2021-001592Current state of cardiac troponin testing in Duchenne muscular dystrophy cardiomyopathy: review and recommendations from the Parent Project Muscular Dystrophy expert panelChristopher F Spurney0Lawrence Charnas1Linda Cripe2Kan Hor3Nicholas King4Kathi Kinnett5Elizabeth M McNally6John-Michael Sauer7Lee Sweeney8Chet Villa9Larry W Markham10Children`s National Heart Institute, Children`s National Hospital, Washington, District of Columbia, USAClinical Research Rare Neurology Disease, Pfizer, Cambridge, Massachusetts, USAThe Heart Center, Nationwide Children`s Hospital, Columbus, Ohio, USAThe Heart Center, Nationwide Children`s Hospital, Columbus, Ohio, USACritical Path Institute, Tucson, Arizona, USAParent Project Muscular Dystrophy, Hackensack, New Jersey, USACenter for Genetic Medicine, Northwestern Medicine, Chicago, Illinois, USACritical Path Institute, Tucson, Arizona, USADepartment of Pharmacology and Therapeutics, University of Florida, Gainesville, Florida, USACardiology, Cincinnati Children`s Hospital Medical Center, Cincinnati, Ohio, USAPediatrics, Division of Pediatric Cardiology, Riley Hospital for Children at Indiana University Health, Indianapolis, Indiana, USACardiac disease is now the leading cause of death in Duchenne muscular dystrophy (DMD). Clinical evaluations over time have demonstrated asymptomatic cardiac troponin elevations and acute elevations are associated with symptoms and cardiac dysfunction in DMD. Clinicians require a better understanding of the relationship of symptoms, troponin levels and progression of cardiac disease in DMD. As clinical trials begin to assess novel cardiac therapeutics in DMD, troponin levels in DMD are important for safety monitoring and outcome measures. The Parent Project Muscular Dystrophy convened an expert panel of cardiologists, scientists, and regulatory and industry specialists on 16 December 2019 in Silver Spring, Maryland and reviewed published and unpublished data from their institutions. The panel recommended retrospective troponin data analyses, prospective longitudinal troponin collection using high-sensitivity cardiac troponin I assays, inclusion of troponin in future clinical trial outcomes and future development of clinical guidelines for monitoring and treating troponin elevations in DMD.https://openheart.bmj.com/content/8/1/e001592.full
spellingShingle Christopher F Spurney
Lawrence Charnas
Linda Cripe
Kan Hor
Nicholas King
Kathi Kinnett
Elizabeth M McNally
John-Michael Sauer
Lee Sweeney
Chet Villa
Larry W Markham
Current state of cardiac troponin testing in Duchenne muscular dystrophy cardiomyopathy: review and recommendations from the Parent Project Muscular Dystrophy expert panel
Open Heart
title Current state of cardiac troponin testing in Duchenne muscular dystrophy cardiomyopathy: review and recommendations from the Parent Project Muscular Dystrophy expert panel
title_full Current state of cardiac troponin testing in Duchenne muscular dystrophy cardiomyopathy: review and recommendations from the Parent Project Muscular Dystrophy expert panel
title_fullStr Current state of cardiac troponin testing in Duchenne muscular dystrophy cardiomyopathy: review and recommendations from the Parent Project Muscular Dystrophy expert panel
title_full_unstemmed Current state of cardiac troponin testing in Duchenne muscular dystrophy cardiomyopathy: review and recommendations from the Parent Project Muscular Dystrophy expert panel
title_short Current state of cardiac troponin testing in Duchenne muscular dystrophy cardiomyopathy: review and recommendations from the Parent Project Muscular Dystrophy expert panel
title_sort current state of cardiac troponin testing in duchenne muscular dystrophy cardiomyopathy review and recommendations from the parent project muscular dystrophy expert panel
url https://openheart.bmj.com/content/8/1/e001592.full
work_keys_str_mv AT christopherfspurney currentstateofcardiactroponintestinginduchennemusculardystrophycardiomyopathyreviewandrecommendationsfromtheparentprojectmusculardystrophyexpertpanel
AT lawrencecharnas currentstateofcardiactroponintestinginduchennemusculardystrophycardiomyopathyreviewandrecommendationsfromtheparentprojectmusculardystrophyexpertpanel
AT lindacripe currentstateofcardiactroponintestinginduchennemusculardystrophycardiomyopathyreviewandrecommendationsfromtheparentprojectmusculardystrophyexpertpanel
AT kanhor currentstateofcardiactroponintestinginduchennemusculardystrophycardiomyopathyreviewandrecommendationsfromtheparentprojectmusculardystrophyexpertpanel
AT nicholasking currentstateofcardiactroponintestinginduchennemusculardystrophycardiomyopathyreviewandrecommendationsfromtheparentprojectmusculardystrophyexpertpanel
AT kathikinnett currentstateofcardiactroponintestinginduchennemusculardystrophycardiomyopathyreviewandrecommendationsfromtheparentprojectmusculardystrophyexpertpanel
AT elizabethmmcnally currentstateofcardiactroponintestinginduchennemusculardystrophycardiomyopathyreviewandrecommendationsfromtheparentprojectmusculardystrophyexpertpanel
AT johnmichaelsauer currentstateofcardiactroponintestinginduchennemusculardystrophycardiomyopathyreviewandrecommendationsfromtheparentprojectmusculardystrophyexpertpanel
AT leesweeney currentstateofcardiactroponintestinginduchennemusculardystrophycardiomyopathyreviewandrecommendationsfromtheparentprojectmusculardystrophyexpertpanel
AT chetvilla currentstateofcardiactroponintestinginduchennemusculardystrophycardiomyopathyreviewandrecommendationsfromtheparentprojectmusculardystrophyexpertpanel
AT larrywmarkham currentstateofcardiactroponintestinginduchennemusculardystrophycardiomyopathyreviewandrecommendationsfromtheparentprojectmusculardystrophyexpertpanel