Diffuse Pulmonary Lymphangiomatosis
Diffuse pulmonary lymphangiomatosis (DPL) is a rare disease characterized by infiltration of the lung, pleura and mediastinum with thin-walled lymphangiomas. DPL can result in mass effect from infiltrative disease, restrictive and obstructive pulmonary physiology, chylous effusions and respiratory f...
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Format: | Article |
Language: | English |
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Wiley
2013-01-01
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Series: | Canadian Respiratory Journal |
Online Access: | http://dx.doi.org/10.1155/2013/971350 |
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author | Kunal C Kadakia Sandeep M Patel Eunhee S Yi Andrew H Limper |
author_facet | Kunal C Kadakia Sandeep M Patel Eunhee S Yi Andrew H Limper |
author_sort | Kunal C Kadakia |
collection | DOAJ |
description | Diffuse pulmonary lymphangiomatosis (DPL) is a rare disease characterized by infiltration of the lung, pleura and mediastinum with thin-walled lymphangiomas. DPL can result in mass effect from infiltrative disease, restrictive and obstructive pulmonary physiology, chylous effusions and respiratory failure. The present article discusses clinical, radiographic and pathological features, and treatment options for DPL. |
format | Article |
id | doaj-art-e93be2d177094429a7b77cc1347a9d51 |
institution | Kabale University |
issn | 1198-2241 |
language | English |
publishDate | 2013-01-01 |
publisher | Wiley |
record_format | Article |
series | Canadian Respiratory Journal |
spelling | doaj-art-e93be2d177094429a7b77cc1347a9d512025-02-03T05:47:21ZengWileyCanadian Respiratory Journal1198-22412013-01-01201525410.1155/2013/971350Diffuse Pulmonary LymphangiomatosisKunal C Kadakia0Sandeep M Patel1Eunhee S Yi2Andrew H Limper3Division of Internal Medicine, Mayo Clinic, Rochester, Minnesota, USADivision of Internal Medicine, Mayo Clinic, Rochester, Minnesota, USADepartment of Anatomic Pathology, Mayo Clinic, Rochester, Minnesota, USADivision of Pulmonary and Critical Care Medicine, Mayo Clinic, Rochester, Minnesota, USADiffuse pulmonary lymphangiomatosis (DPL) is a rare disease characterized by infiltration of the lung, pleura and mediastinum with thin-walled lymphangiomas. DPL can result in mass effect from infiltrative disease, restrictive and obstructive pulmonary physiology, chylous effusions and respiratory failure. The present article discusses clinical, radiographic and pathological features, and treatment options for DPL.http://dx.doi.org/10.1155/2013/971350 |
spellingShingle | Kunal C Kadakia Sandeep M Patel Eunhee S Yi Andrew H Limper Diffuse Pulmonary Lymphangiomatosis Canadian Respiratory Journal |
title | Diffuse Pulmonary Lymphangiomatosis |
title_full | Diffuse Pulmonary Lymphangiomatosis |
title_fullStr | Diffuse Pulmonary Lymphangiomatosis |
title_full_unstemmed | Diffuse Pulmonary Lymphangiomatosis |
title_short | Diffuse Pulmonary Lymphangiomatosis |
title_sort | diffuse pulmonary lymphangiomatosis |
url | http://dx.doi.org/10.1155/2013/971350 |
work_keys_str_mv | AT kunalckadakia diffusepulmonarylymphangiomatosis AT sandeepmpatel diffusepulmonarylymphangiomatosis AT eunheesyi diffusepulmonarylymphangiomatosis AT andrewhlimper diffusepulmonarylymphangiomatosis |