Diffuse Pulmonary Lymphangiomatosis

Diffuse pulmonary lymphangiomatosis (DPL) is a rare disease characterized by infiltration of the lung, pleura and mediastinum with thin-walled lymphangiomas. DPL can result in mass effect from infiltrative disease, restrictive and obstructive pulmonary physiology, chylous effusions and respiratory f...

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Main Authors: Kunal C Kadakia, Sandeep M Patel, Eunhee S Yi, Andrew H Limper
Format: Article
Language:English
Published: Wiley 2013-01-01
Series:Canadian Respiratory Journal
Online Access:http://dx.doi.org/10.1155/2013/971350
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author Kunal C Kadakia
Sandeep M Patel
Eunhee S Yi
Andrew H Limper
author_facet Kunal C Kadakia
Sandeep M Patel
Eunhee S Yi
Andrew H Limper
author_sort Kunal C Kadakia
collection DOAJ
description Diffuse pulmonary lymphangiomatosis (DPL) is a rare disease characterized by infiltration of the lung, pleura and mediastinum with thin-walled lymphangiomas. DPL can result in mass effect from infiltrative disease, restrictive and obstructive pulmonary physiology, chylous effusions and respiratory failure. The present article discusses clinical, radiographic and pathological features, and treatment options for DPL.
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institution Kabale University
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publishDate 2013-01-01
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series Canadian Respiratory Journal
spelling doaj-art-e93be2d177094429a7b77cc1347a9d512025-02-03T05:47:21ZengWileyCanadian Respiratory Journal1198-22412013-01-01201525410.1155/2013/971350Diffuse Pulmonary LymphangiomatosisKunal C Kadakia0Sandeep M Patel1Eunhee S Yi2Andrew H Limper3Division of Internal Medicine, Mayo Clinic, Rochester, Minnesota, USADivision of Internal Medicine, Mayo Clinic, Rochester, Minnesota, USADepartment of Anatomic Pathology, Mayo Clinic, Rochester, Minnesota, USADivision of Pulmonary and Critical Care Medicine, Mayo Clinic, Rochester, Minnesota, USADiffuse pulmonary lymphangiomatosis (DPL) is a rare disease characterized by infiltration of the lung, pleura and mediastinum with thin-walled lymphangiomas. DPL can result in mass effect from infiltrative disease, restrictive and obstructive pulmonary physiology, chylous effusions and respiratory failure. The present article discusses clinical, radiographic and pathological features, and treatment options for DPL.http://dx.doi.org/10.1155/2013/971350
spellingShingle Kunal C Kadakia
Sandeep M Patel
Eunhee S Yi
Andrew H Limper
Diffuse Pulmonary Lymphangiomatosis
Canadian Respiratory Journal
title Diffuse Pulmonary Lymphangiomatosis
title_full Diffuse Pulmonary Lymphangiomatosis
title_fullStr Diffuse Pulmonary Lymphangiomatosis
title_full_unstemmed Diffuse Pulmonary Lymphangiomatosis
title_short Diffuse Pulmonary Lymphangiomatosis
title_sort diffuse pulmonary lymphangiomatosis
url http://dx.doi.org/10.1155/2013/971350
work_keys_str_mv AT kunalckadakia diffusepulmonarylymphangiomatosis
AT sandeepmpatel diffusepulmonarylymphangiomatosis
AT eunheesyi diffusepulmonarylymphangiomatosis
AT andrewhlimper diffusepulmonarylymphangiomatosis