A Rare Case of Nevus Spilus Type of Giant Congenital Melanocytic Nevus with Classic Proliferative Nodules, Intraparenchymal Melanosis, and Seizures

Congenital melanocytic nevi, as the name suggests, are present since birth. They are called giant congenital melanocytic nevus (GCMN) when the size exceeds >20 cm in diameter. Due to its unsightly appearance, there is major psychosocial impact on the patient and the family. GCMN in due course of...

Full description

Saved in:
Bibliographic Details
Main Authors: Pankaj Das, Biju Vasudevan, Ahmed Waheed Kashif, Lekshmi Priya Krishnan, Anand Mannu, Abhinav Kumar Verma, Shweta Pandey
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2024-12-01
Series:Indian Journal of Paediatric Dermatology
Subjects:
Online Access:https://journals.lww.com/10.4103/ijpd.ijpd_91_24
Tags: Add Tag
No Tags, Be the first to tag this record!
_version_ 1841550067700334592
author Pankaj Das
Biju Vasudevan
Ahmed Waheed Kashif
Lekshmi Priya Krishnan
Anand Mannu
Abhinav Kumar Verma
Shweta Pandey
author_facet Pankaj Das
Biju Vasudevan
Ahmed Waheed Kashif
Lekshmi Priya Krishnan
Anand Mannu
Abhinav Kumar Verma
Shweta Pandey
author_sort Pankaj Das
collection DOAJ
description Congenital melanocytic nevi, as the name suggests, are present since birth. They are called giant congenital melanocytic nevus (GCMN) when the size exceeds >20 cm in diameter. Due to its unsightly appearance, there is major psychosocial impact on the patient and the family. GCMN in due course of time may give rise to malignant melanoma not only in the GCMN but also in the leptomeninges. Clinical variants of GCMN include nevus spilus type, which is a rare variant. In addition to that with time, GCMN may continue to be affected with benign nodules. We present a rare case of a nevus spilus type of GCMN with classic proliferative nodules associated with intraparenchymal melanosis in brain, leading to seizures.
format Article
id doaj-art-df8c631bd245412db0901921c512021c
institution Kabale University
issn 2319-7250
2319-7269
language English
publishDate 2024-12-01
publisher Wolters Kluwer Medknow Publications
record_format Article
series Indian Journal of Paediatric Dermatology
spelling doaj-art-df8c631bd245412db0901921c512021c2025-01-10T10:02:14ZengWolters Kluwer Medknow PublicationsIndian Journal of Paediatric Dermatology2319-72502319-72692024-12-0125432532810.4103/ijpd.ijpd_91_24A Rare Case of Nevus Spilus Type of Giant Congenital Melanocytic Nevus with Classic Proliferative Nodules, Intraparenchymal Melanosis, and SeizuresPankaj DasBiju VasudevanAhmed Waheed KashifLekshmi Priya KrishnanAnand MannuAbhinav Kumar VermaShweta PandeyCongenital melanocytic nevi, as the name suggests, are present since birth. They are called giant congenital melanocytic nevus (GCMN) when the size exceeds >20 cm in diameter. Due to its unsightly appearance, there is major psychosocial impact on the patient and the family. GCMN in due course of time may give rise to malignant melanoma not only in the GCMN but also in the leptomeninges. Clinical variants of GCMN include nevus spilus type, which is a rare variant. In addition to that with time, GCMN may continue to be affected with benign nodules. We present a rare case of a nevus spilus type of GCMN with classic proliferative nodules associated with intraparenchymal melanosis in brain, leading to seizures.https://journals.lww.com/10.4103/ijpd.ijpd_91_24bathing trunk nevusbenignclassic proliferative nodulesdiffuse neuroid proliferationsgiant congenital melanocytic nevusleptomeningeal melanocytosismalignantmelanomanevus spilusseizures
spellingShingle Pankaj Das
Biju Vasudevan
Ahmed Waheed Kashif
Lekshmi Priya Krishnan
Anand Mannu
Abhinav Kumar Verma
Shweta Pandey
A Rare Case of Nevus Spilus Type of Giant Congenital Melanocytic Nevus with Classic Proliferative Nodules, Intraparenchymal Melanosis, and Seizures
Indian Journal of Paediatric Dermatology
bathing trunk nevus
benign
classic proliferative nodules
diffuse neuroid proliferations
giant congenital melanocytic nevus
leptomeningeal melanocytosis
malignant
melanoma
nevus spilus
seizures
title A Rare Case of Nevus Spilus Type of Giant Congenital Melanocytic Nevus with Classic Proliferative Nodules, Intraparenchymal Melanosis, and Seizures
title_full A Rare Case of Nevus Spilus Type of Giant Congenital Melanocytic Nevus with Classic Proliferative Nodules, Intraparenchymal Melanosis, and Seizures
title_fullStr A Rare Case of Nevus Spilus Type of Giant Congenital Melanocytic Nevus with Classic Proliferative Nodules, Intraparenchymal Melanosis, and Seizures
title_full_unstemmed A Rare Case of Nevus Spilus Type of Giant Congenital Melanocytic Nevus with Classic Proliferative Nodules, Intraparenchymal Melanosis, and Seizures
title_short A Rare Case of Nevus Spilus Type of Giant Congenital Melanocytic Nevus with Classic Proliferative Nodules, Intraparenchymal Melanosis, and Seizures
title_sort rare case of nevus spilus type of giant congenital melanocytic nevus with classic proliferative nodules intraparenchymal melanosis and seizures
topic bathing trunk nevus
benign
classic proliferative nodules
diffuse neuroid proliferations
giant congenital melanocytic nevus
leptomeningeal melanocytosis
malignant
melanoma
nevus spilus
seizures
url https://journals.lww.com/10.4103/ijpd.ijpd_91_24
work_keys_str_mv AT pankajdas ararecaseofnevusspilustypeofgiantcongenitalmelanocyticnevuswithclassicproliferativenodulesintraparenchymalmelanosisandseizures
AT bijuvasudevan ararecaseofnevusspilustypeofgiantcongenitalmelanocyticnevuswithclassicproliferativenodulesintraparenchymalmelanosisandseizures
AT ahmedwaheedkashif ararecaseofnevusspilustypeofgiantcongenitalmelanocyticnevuswithclassicproliferativenodulesintraparenchymalmelanosisandseizures
AT lekshmipriyakrishnan ararecaseofnevusspilustypeofgiantcongenitalmelanocyticnevuswithclassicproliferativenodulesintraparenchymalmelanosisandseizures
AT anandmannu ararecaseofnevusspilustypeofgiantcongenitalmelanocyticnevuswithclassicproliferativenodulesintraparenchymalmelanosisandseizures
AT abhinavkumarverma ararecaseofnevusspilustypeofgiantcongenitalmelanocyticnevuswithclassicproliferativenodulesintraparenchymalmelanosisandseizures
AT shwetapandey ararecaseofnevusspilustypeofgiantcongenitalmelanocyticnevuswithclassicproliferativenodulesintraparenchymalmelanosisandseizures
AT pankajdas rarecaseofnevusspilustypeofgiantcongenitalmelanocyticnevuswithclassicproliferativenodulesintraparenchymalmelanosisandseizures
AT bijuvasudevan rarecaseofnevusspilustypeofgiantcongenitalmelanocyticnevuswithclassicproliferativenodulesintraparenchymalmelanosisandseizures
AT ahmedwaheedkashif rarecaseofnevusspilustypeofgiantcongenitalmelanocyticnevuswithclassicproliferativenodulesintraparenchymalmelanosisandseizures
AT lekshmipriyakrishnan rarecaseofnevusspilustypeofgiantcongenitalmelanocyticnevuswithclassicproliferativenodulesintraparenchymalmelanosisandseizures
AT anandmannu rarecaseofnevusspilustypeofgiantcongenitalmelanocyticnevuswithclassicproliferativenodulesintraparenchymalmelanosisandseizures
AT abhinavkumarverma rarecaseofnevusspilustypeofgiantcongenitalmelanocyticnevuswithclassicproliferativenodulesintraparenchymalmelanosisandseizures
AT shwetapandey rarecaseofnevusspilustypeofgiantcongenitalmelanocyticnevuswithclassicproliferativenodulesintraparenchymalmelanosisandseizures