Granulomatosis with polyangiitis mimicking multisystem pyoderma gangrenosum: A case report
Granulomatosis with polyangiitis, a type of small-medium vessel vasculitis, can pose diagnostic challenges due to its diverse clinical manifestations. We present a case that mimicked multisystem pyoderma gangrenosum with cutaneous ulceration, renal sparing, and antineutrophil cytoplasmic antibody ne...
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| Format: | Article |
| Language: | English |
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SAGE Publishing
2024-12-01
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| Series: | SAGE Open Medical Case Reports |
| Online Access: | https://doi.org/10.1177/2050313X241304229 |
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| _version_ | 1846127774390026240 |
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| author | Amanda Gormley Peter Green |
| author_facet | Amanda Gormley Peter Green |
| author_sort | Amanda Gormley |
| collection | DOAJ |
| description | Granulomatosis with polyangiitis, a type of small-medium vessel vasculitis, can pose diagnostic challenges due to its diverse clinical manifestations. We present a case that mimicked multisystem pyoderma gangrenosum with cutaneous ulceration, renal sparing, and antineutrophil cytoplasmic antibody negativity. Although antineutrophil cytoplasmic antibody is positive in approximately 90% of cases of granulomatosis with polyangiitis, its negativity should not exclude the diagnosis. Additionally, pyoderma gangrenosum-like cutaneous ulcers should prompt consideration of granulomatosis with polyangiitis, especially in the context of multisystem disease presentation. This case underscores the importance of maintaining a high suspicion for granulomatosis with polyangiitis in patients presenting with cutaneous ulceration and respiratory tract disease. |
| format | Article |
| id | doaj-art-ddebdf416be446cbb9ed7075f6534863 |
| institution | Kabale University |
| issn | 2050-313X |
| language | English |
| publishDate | 2024-12-01 |
| publisher | SAGE Publishing |
| record_format | Article |
| series | SAGE Open Medical Case Reports |
| spelling | doaj-art-ddebdf416be446cbb9ed7075f65348632024-12-11T11:03:26ZengSAGE PublishingSAGE Open Medical Case Reports2050-313X2024-12-011210.1177/2050313X241304229Granulomatosis with polyangiitis mimicking multisystem pyoderma gangrenosum: A case reportAmanda Gormley0Peter Green1Faculty of Medicine, Dalhousie University, Halifax, NS, CanadaDivision of Clinical Dermatology and Cutaneous Science, Department of Medicine, Dalhousie University, Halifax, NS, CanadaGranulomatosis with polyangiitis, a type of small-medium vessel vasculitis, can pose diagnostic challenges due to its diverse clinical manifestations. We present a case that mimicked multisystem pyoderma gangrenosum with cutaneous ulceration, renal sparing, and antineutrophil cytoplasmic antibody negativity. Although antineutrophil cytoplasmic antibody is positive in approximately 90% of cases of granulomatosis with polyangiitis, its negativity should not exclude the diagnosis. Additionally, pyoderma gangrenosum-like cutaneous ulcers should prompt consideration of granulomatosis with polyangiitis, especially in the context of multisystem disease presentation. This case underscores the importance of maintaining a high suspicion for granulomatosis with polyangiitis in patients presenting with cutaneous ulceration and respiratory tract disease.https://doi.org/10.1177/2050313X241304229 |
| spellingShingle | Amanda Gormley Peter Green Granulomatosis with polyangiitis mimicking multisystem pyoderma gangrenosum: A case report SAGE Open Medical Case Reports |
| title | Granulomatosis with polyangiitis mimicking multisystem pyoderma gangrenosum: A case report |
| title_full | Granulomatosis with polyangiitis mimicking multisystem pyoderma gangrenosum: A case report |
| title_fullStr | Granulomatosis with polyangiitis mimicking multisystem pyoderma gangrenosum: A case report |
| title_full_unstemmed | Granulomatosis with polyangiitis mimicking multisystem pyoderma gangrenosum: A case report |
| title_short | Granulomatosis with polyangiitis mimicking multisystem pyoderma gangrenosum: A case report |
| title_sort | granulomatosis with polyangiitis mimicking multisystem pyoderma gangrenosum a case report |
| url | https://doi.org/10.1177/2050313X241304229 |
| work_keys_str_mv | AT amandagormley granulomatosiswithpolyangiitismimickingmultisystempyodermagangrenosumacasereport AT petergreen granulomatosiswithpolyangiitismimickingmultisystempyodermagangrenosumacasereport |