Discordant Response to Nivolumab Plus Ipilimumab and Identification of BRAF V600E Mutation in Biphasic Malignant Pleural Mesothelioma: Case Report

Therapeutic advancement for malignant pleural mesothelioma (MPM) has been limited. Combination immunotherapy with nivolumab plus ipilimumab is a frontline treatment option for advanced MPM that is typically deployed for patients with sarcomatoid or biphasic MPM. Here, we present a case of biphasic M...

Full description

Saved in:
Bibliographic Details
Main Authors: Olivia Wilkins, DO, Adedamola Omogbehin, MD, Peter J. Bergquist, MD, Chul Kim, MD, MPH, Stephen V. Liu, MD, Joshua E. Reuss, MD
Format: Article
Language:English
Published: Elsevier 2025-05-01
Series:JTO Clinical and Research Reports
Subjects:
Online Access:http://www.sciencedirect.com/science/article/pii/S2666364325000360
Tags: Add Tag
No Tags, Be the first to tag this record!
_version_ 1849322057231237120
author Olivia Wilkins, DO
Adedamola Omogbehin, MD
Peter J. Bergquist, MD
Chul Kim, MD, MPH
Stephen V. Liu, MD
Joshua E. Reuss, MD
author_facet Olivia Wilkins, DO
Adedamola Omogbehin, MD
Peter J. Bergquist, MD
Chul Kim, MD, MPH
Stephen V. Liu, MD
Joshua E. Reuss, MD
author_sort Olivia Wilkins, DO
collection DOAJ
description Therapeutic advancement for malignant pleural mesothelioma (MPM) has been limited. Combination immunotherapy with nivolumab plus ipilimumab is a frontline treatment option for advanced MPM that is typically deployed for patients with sarcomatoid or biphasic MPM. Here, we present a case of biphasic MPM that exhibited a unique response pattern to first-line treatment with nivolumab plus ipilimumab, with brisk response in pleural and mediastinal sites of disease, but rapid progression in osseous/soft tissue sites of disease complicated by pathologic spinal cord compression. Pathologic findings from bony metastasis at progression found pure epithelioid histology without any evidence of sarcomatoid differentiation. Next-generation sequencing of this specimen revealed a BRAF V600E mutation, and the patient was subsequently treated with dabrafenib plus trametinib, achieving ongoing clinical and imaging response in all sites of the disease, including bones. This case supports the use of next-generation sequencing profiling in MPM, particularly in circumstances in which novel discordant response patterns are observed.
format Article
id doaj-art-cfe08f8f98a1443ea0d9bc8f91d4ab2d
institution Kabale University
issn 2666-3643
language English
publishDate 2025-05-01
publisher Elsevier
record_format Article
series JTO Clinical and Research Reports
spelling doaj-art-cfe08f8f98a1443ea0d9bc8f91d4ab2d2025-08-20T03:49:33ZengElsevierJTO Clinical and Research Reports2666-36432025-05-016510082010.1016/j.jtocrr.2025.100820Discordant Response to Nivolumab Plus Ipilimumab and Identification of BRAF V600E Mutation in Biphasic Malignant Pleural Mesothelioma: Case ReportOlivia Wilkins, DO0Adedamola Omogbehin, MD1Peter J. Bergquist, MD2Chul Kim, MD, MPH3Stephen V. Liu, MD4Joshua E. Reuss, MD5Lombardi Comprehensive Cancer Center, Georgetown University, Washington, DCDepartment of Radiation Oncology, MedStar Washington Hospital Center, Washington, DCDepartment of Radiology, Georgetown University, Washington, DCLombardi Comprehensive Cancer Center, Georgetown University, Washington, DCLombardi Comprehensive Cancer Center, Georgetown University, Washington, DCLombardi Comprehensive Cancer Center, Georgetown University, Washington, DC; Corresponding author. Address for correspondence: Joshua E. Reuss, MD, Georgetown Lombardi Comprehensive Cancer Center, Lombardi Cancer Center Podium B, 3800 Reservoir Rd NW, Washington, DC 20007.Therapeutic advancement for malignant pleural mesothelioma (MPM) has been limited. Combination immunotherapy with nivolumab plus ipilimumab is a frontline treatment option for advanced MPM that is typically deployed for patients with sarcomatoid or biphasic MPM. Here, we present a case of biphasic MPM that exhibited a unique response pattern to first-line treatment with nivolumab plus ipilimumab, with brisk response in pleural and mediastinal sites of disease, but rapid progression in osseous/soft tissue sites of disease complicated by pathologic spinal cord compression. Pathologic findings from bony metastasis at progression found pure epithelioid histology without any evidence of sarcomatoid differentiation. Next-generation sequencing of this specimen revealed a BRAF V600E mutation, and the patient was subsequently treated with dabrafenib plus trametinib, achieving ongoing clinical and imaging response in all sites of the disease, including bones. This case supports the use of next-generation sequencing profiling in MPM, particularly in circumstances in which novel discordant response patterns are observed.http://www.sciencedirect.com/science/article/pii/S2666364325000360Case reportMalignant pleural mesotheliomaBRAF V600EDabrafenibTrametinib
spellingShingle Olivia Wilkins, DO
Adedamola Omogbehin, MD
Peter J. Bergquist, MD
Chul Kim, MD, MPH
Stephen V. Liu, MD
Joshua E. Reuss, MD
Discordant Response to Nivolumab Plus Ipilimumab and Identification of BRAF V600E Mutation in Biphasic Malignant Pleural Mesothelioma: Case Report
JTO Clinical and Research Reports
Case report
Malignant pleural mesothelioma
BRAF V600E
Dabrafenib
Trametinib
title Discordant Response to Nivolumab Plus Ipilimumab and Identification of BRAF V600E Mutation in Biphasic Malignant Pleural Mesothelioma: Case Report
title_full Discordant Response to Nivolumab Plus Ipilimumab and Identification of BRAF V600E Mutation in Biphasic Malignant Pleural Mesothelioma: Case Report
title_fullStr Discordant Response to Nivolumab Plus Ipilimumab and Identification of BRAF V600E Mutation in Biphasic Malignant Pleural Mesothelioma: Case Report
title_full_unstemmed Discordant Response to Nivolumab Plus Ipilimumab and Identification of BRAF V600E Mutation in Biphasic Malignant Pleural Mesothelioma: Case Report
title_short Discordant Response to Nivolumab Plus Ipilimumab and Identification of BRAF V600E Mutation in Biphasic Malignant Pleural Mesothelioma: Case Report
title_sort discordant response to nivolumab plus ipilimumab and identification of braf v600e mutation in biphasic malignant pleural mesothelioma case report
topic Case report
Malignant pleural mesothelioma
BRAF V600E
Dabrafenib
Trametinib
url http://www.sciencedirect.com/science/article/pii/S2666364325000360
work_keys_str_mv AT oliviawilkinsdo discordantresponsetonivolumabplusipilimumabandidentificationofbrafv600emutationinbiphasicmalignantpleuralmesotheliomacasereport
AT adedamolaomogbehinmd discordantresponsetonivolumabplusipilimumabandidentificationofbrafv600emutationinbiphasicmalignantpleuralmesotheliomacasereport
AT peterjbergquistmd discordantresponsetonivolumabplusipilimumabandidentificationofbrafv600emutationinbiphasicmalignantpleuralmesotheliomacasereport
AT chulkimmdmph discordantresponsetonivolumabplusipilimumabandidentificationofbrafv600emutationinbiphasicmalignantpleuralmesotheliomacasereport
AT stephenvliumd discordantresponsetonivolumabplusipilimumabandidentificationofbrafv600emutationinbiphasicmalignantpleuralmesotheliomacasereport
AT joshuaereussmd discordantresponsetonivolumabplusipilimumabandidentificationofbrafv600emutationinbiphasicmalignantpleuralmesotheliomacasereport