MJF-14 proximity ligation assay detects early non-inclusion alpha-synuclein pathology with enhanced specificity and sensitivity

Abstract α-Synuclein proximity ligation assay (PLA) has proved a sensitive technique for detection of non-Lewy body α-synuclein aggregate pathology. Here, we describe the MJF-14 PLA, a new PLA towards aggregated α-synuclein with unprecedented specificity, using the aggregate-selective α-synuclein an...

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Main Authors: Nanna Møller Jensen, YuHong Fu, Cristine Betzer, Hongyun Li, Sara Elfarrash, Ali H. Shaib, Donatus Krah, Zagorka Vitic, Lasse Reimer, Hjalte Gram, Vladimir Buchman, Mark Denham, Silvio O. Rizzoli, Glenda M. Halliday, Poul Henning Jensen
Format: Article
Language:English
Published: Nature Portfolio 2024-11-01
Series:npj Parkinson's Disease
Online Access:https://doi.org/10.1038/s41531-024-00841-9
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author Nanna Møller Jensen
YuHong Fu
Cristine Betzer
Hongyun Li
Sara Elfarrash
Ali H. Shaib
Donatus Krah
Zagorka Vitic
Lasse Reimer
Hjalte Gram
Vladimir Buchman
Mark Denham
Silvio O. Rizzoli
Glenda M. Halliday
Poul Henning Jensen
author_facet Nanna Møller Jensen
YuHong Fu
Cristine Betzer
Hongyun Li
Sara Elfarrash
Ali H. Shaib
Donatus Krah
Zagorka Vitic
Lasse Reimer
Hjalte Gram
Vladimir Buchman
Mark Denham
Silvio O. Rizzoli
Glenda M. Halliday
Poul Henning Jensen
author_sort Nanna Møller Jensen
collection DOAJ
description Abstract α-Synuclein proximity ligation assay (PLA) has proved a sensitive technique for detection of non-Lewy body α-synuclein aggregate pathology. Here, we describe the MJF-14 PLA, a new PLA towards aggregated α-synuclein with unprecedented specificity, using the aggregate-selective α-synuclein antibody MJFR-14-6-4-2 (hereafter MJF-14). Signal in the assay correlates with α-synuclein aggregation in cell culture and human neurons, induced by α-synuclein overexpression or pre-formed fibrils. Co-labelling of MJF-14 PLA and pS129-α-synuclein immunofluorescence in post-mortem cases of dementia with Lewy bodies shows that while the MJF-14 PLA reveals extensive non-inclusion pathology, it is not sensitive towards pS129-α-synuclein-positive Lewy bodies. In Parkinson’s disease brain, direct comparison of PLA and immunohistochemistry with the MJF-14 antibody shows widespread α-synuclein pathology preceding the formation of conventional Lewy pathology. In conclusion, we introduce an improved α-synuclein aggregate PLA to uncover abundant non-inclusion pathology, which deserves future validation with brain bank resources and in different synucleinopathies.
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spelling doaj-art-c55cdec6dd264aa8b793c43fcfeb00132024-12-01T12:15:05ZengNature Portfolionpj Parkinson's Disease2373-80572024-11-0110112110.1038/s41531-024-00841-9MJF-14 proximity ligation assay detects early non-inclusion alpha-synuclein pathology with enhanced specificity and sensitivityNanna Møller Jensen0YuHong Fu1Cristine Betzer2Hongyun Li3Sara Elfarrash4Ali H. Shaib5Donatus Krah6Zagorka Vitic7Lasse Reimer8Hjalte Gram9Vladimir Buchman10Mark Denham11Silvio O. Rizzoli12Glenda M. Halliday13Poul Henning Jensen14DANDRITE - Danish Research Institute of Translational NeuroscienceBrain and Mind Centre & Faculty of Medicine and Health, School of Medical Sciences, University of SydneyDANDRITE - Danish Research Institute of Translational NeuroscienceBrain and Mind Centre & Faculty of Medicine and Health, School of Medical Sciences, University of SydneyDANDRITE - Danish Research Institute of Translational NeuroscienceDepartment of Neuro- and Sensory Physiology, University Medical Center GöttingenDepartment of Neuro- and Sensory Physiology, University Medical Center GöttingenDANDRITE - Danish Research Institute of Translational NeuroscienceDANDRITE - Danish Research Institute of Translational NeuroscienceDANDRITE - Danish Research Institute of Translational NeuroscienceSchool of Biosciences, Cardiff UniversityDANDRITE - Danish Research Institute of Translational NeuroscienceDepartment of Neuro- and Sensory Physiology, University Medical Center GöttingenBrain and Mind Centre & Faculty of Medicine and Health, School of Medical Sciences, University of SydneyDANDRITE - Danish Research Institute of Translational NeuroscienceAbstract α-Synuclein proximity ligation assay (PLA) has proved a sensitive technique for detection of non-Lewy body α-synuclein aggregate pathology. Here, we describe the MJF-14 PLA, a new PLA towards aggregated α-synuclein with unprecedented specificity, using the aggregate-selective α-synuclein antibody MJFR-14-6-4-2 (hereafter MJF-14). Signal in the assay correlates with α-synuclein aggregation in cell culture and human neurons, induced by α-synuclein overexpression or pre-formed fibrils. Co-labelling of MJF-14 PLA and pS129-α-synuclein immunofluorescence in post-mortem cases of dementia with Lewy bodies shows that while the MJF-14 PLA reveals extensive non-inclusion pathology, it is not sensitive towards pS129-α-synuclein-positive Lewy bodies. In Parkinson’s disease brain, direct comparison of PLA and immunohistochemistry with the MJF-14 antibody shows widespread α-synuclein pathology preceding the formation of conventional Lewy pathology. In conclusion, we introduce an improved α-synuclein aggregate PLA to uncover abundant non-inclusion pathology, which deserves future validation with brain bank resources and in different synucleinopathies.https://doi.org/10.1038/s41531-024-00841-9
spellingShingle Nanna Møller Jensen
YuHong Fu
Cristine Betzer
Hongyun Li
Sara Elfarrash
Ali H. Shaib
Donatus Krah
Zagorka Vitic
Lasse Reimer
Hjalte Gram
Vladimir Buchman
Mark Denham
Silvio O. Rizzoli
Glenda M. Halliday
Poul Henning Jensen
MJF-14 proximity ligation assay detects early non-inclusion alpha-synuclein pathology with enhanced specificity and sensitivity
npj Parkinson's Disease
title MJF-14 proximity ligation assay detects early non-inclusion alpha-synuclein pathology with enhanced specificity and sensitivity
title_full MJF-14 proximity ligation assay detects early non-inclusion alpha-synuclein pathology with enhanced specificity and sensitivity
title_fullStr MJF-14 proximity ligation assay detects early non-inclusion alpha-synuclein pathology with enhanced specificity and sensitivity
title_full_unstemmed MJF-14 proximity ligation assay detects early non-inclusion alpha-synuclein pathology with enhanced specificity and sensitivity
title_short MJF-14 proximity ligation assay detects early non-inclusion alpha-synuclein pathology with enhanced specificity and sensitivity
title_sort mjf 14 proximity ligation assay detects early non inclusion alpha synuclein pathology with enhanced specificity and sensitivity
url https://doi.org/10.1038/s41531-024-00841-9
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