A rare giant renal angiomyolipoma in a 17-year-old male: A case report

Renal angiomyolipoma is an uncommon benign tumor that mostly affects adults and is highly associated with tuberous sclerosis. It's very uncommon for it to affect adolescents. In this case, a 17-year-old male with abdominal pain and distension was diagnosed with sporadic giant renal angiomyolipo...

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Main Authors: Fred Laizer, Hanson Nkini, Heri Babu, Erasto Medard, Amon Bamanyis, Teodros Veronesi
Format: Article
Language:English
Published: Elsevier 2025-01-01
Series:Urology Case Reports
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Online Access:http://www.sciencedirect.com/science/article/pii/S2214442024002419
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author Fred Laizer
Hanson Nkini
Heri Babu
Erasto Medard
Amon Bamanyis
Teodros Veronesi
author_facet Fred Laizer
Hanson Nkini
Heri Babu
Erasto Medard
Amon Bamanyis
Teodros Veronesi
author_sort Fred Laizer
collection DOAJ
description Renal angiomyolipoma is an uncommon benign tumor that mostly affects adults and is highly associated with tuberous sclerosis. It's very uncommon for it to affect adolescents. In this case, a 17-year-old male with abdominal pain and distension was diagnosed with sporadic giant renal angiomyolipoma. Histopathology confirmed the diagnosis after a successful nephrectomy. Though rare in teenagers, giant renal angiomyolipoma can be managed with surgery. Histopathology is a mainstay of confirming the diagnosis. Conclusion: This case highlights the difficulties in managing big retroperitoneal tumors in teenagers and the necessity of taking sporadic angiomyolipoma into account when making a differential diagnosis.
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publishDate 2025-01-01
publisher Elsevier
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series Urology Case Reports
spelling doaj-art-c074a905b2514834829f590d46182e7d2025-01-14T04:12:16ZengElsevierUrology Case Reports2214-44202025-01-0158102887A rare giant renal angiomyolipoma in a 17-year-old male: A case reportFred Laizer0Hanson Nkini1Heri Babu2Erasto Medard3Amon Bamanyis4Teodros Veronesi5Department of General Surgery, Mt Meru Regional Referral Hospital, P.O Box 3092, Arusha, Tanzania; Corresponding author.Department of General Surgery, Mt Meru Regional Referral Hospital, P.O Box 3092, Arusha, TanzaniaDepartment of General Surgery, Mt Meru Regional Referral Hospital, P.O Box 3092, Arusha, TanzaniaDepartment of General Surgery, Mt Meru Regional Referral Hospital, P.O Box 3092, Arusha, TanzaniaDepartment of Histopathology, Mt Meru Regional Referral Hospital, P.O Box 3092, Arusha, TanzaniaDepartment of Histopathology, Mt Meru Regional Referral Hospital, P.O Box 3092, Arusha, TanzaniaRenal angiomyolipoma is an uncommon benign tumor that mostly affects adults and is highly associated with tuberous sclerosis. It's very uncommon for it to affect adolescents. In this case, a 17-year-old male with abdominal pain and distension was diagnosed with sporadic giant renal angiomyolipoma. Histopathology confirmed the diagnosis after a successful nephrectomy. Though rare in teenagers, giant renal angiomyolipoma can be managed with surgery. Histopathology is a mainstay of confirming the diagnosis. Conclusion: This case highlights the difficulties in managing big retroperitoneal tumors in teenagers and the necessity of taking sporadic angiomyolipoma into account when making a differential diagnosis.http://www.sciencedirect.com/science/article/pii/S2214442024002419Renal angiomyolipomaGiant renal angiomyolipomaNephrectomyAdolescent
spellingShingle Fred Laizer
Hanson Nkini
Heri Babu
Erasto Medard
Amon Bamanyis
Teodros Veronesi
A rare giant renal angiomyolipoma in a 17-year-old male: A case report
Urology Case Reports
Renal angiomyolipoma
Giant renal angiomyolipoma
Nephrectomy
Adolescent
title A rare giant renal angiomyolipoma in a 17-year-old male: A case report
title_full A rare giant renal angiomyolipoma in a 17-year-old male: A case report
title_fullStr A rare giant renal angiomyolipoma in a 17-year-old male: A case report
title_full_unstemmed A rare giant renal angiomyolipoma in a 17-year-old male: A case report
title_short A rare giant renal angiomyolipoma in a 17-year-old male: A case report
title_sort rare giant renal angiomyolipoma in a 17 year old male a case report
topic Renal angiomyolipoma
Giant renal angiomyolipoma
Nephrectomy
Adolescent
url http://www.sciencedirect.com/science/article/pii/S2214442024002419
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