Nasal reconstruction using ribs in a patient with Binder syndrome: A case report and literature review

Introduction: Binder’s syndrome can also be known as maxillonasal dysplasia and it is a congenital malformation characterized by nasomaxillary hypoplasia resulting from an underdevelopment of the middle facial skeleton. The current incidence or prevalence is still unknown, but it affects approximate...

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Main Authors: Oona Tomiê Daronch, Renata Fernanda Ramos Marcante, Laisa Brandão Carvalho, Aristides Augusto Palhares
Format: Article
Language:English
Published: Thieme Revinter Publicações Ltda. 2023-09-01
Series:Revista Brasileira de Cirurgia Plástica
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Online Access:http://www.rbcp.org.br/export-pdf/3358/1983-5175-rbcp-38-03-e0786-en.pdf
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author Oona Tomiê Daronch
Renata Fernanda Ramos Marcante
Laisa Brandão Carvalho
Aristides Augusto Palhares
author_facet Oona Tomiê Daronch
Renata Fernanda Ramos Marcante
Laisa Brandão Carvalho
Aristides Augusto Palhares
author_sort Oona Tomiê Daronch
collection DOAJ
description Introduction: Binder’s syndrome can also be known as maxillonasal dysplasia and it is a congenital malformation characterized by nasomaxillary hypoplasia resulting from an underdevelopment of the middle facial skeleton. The current incidence or prevalence is still unknown, but it affects approximately one child in every 10,000 births. The diagnosis can be clinical or associated with prenatal ultrasonography, characterized by a flattened nose and abnormal maxillary convexity. The treatment is surgical to correct aesthetic and functional abnormalities. Case Report: Patient diagnosed with Binder’s syndrome at the age of 14, without other associated malformations, with aesthetic and functional nasal complaints. Surgical correction began with the extraction of a block of the sixth costal cartilage on the left, with a nasal opening on the columellar margin, in the pattern of an open rhinoplasty, and tissue dissection in the sub-SMAS plane. After preparing the nasal receptor area, a block of cartilage was sculpted for reconstruction of the nasal dorsum, alar grafts and septal cartilage grafts. There was an improvement in the projection of the nasal tip and nasal dorsum. Conclusion: Rhinoplasty can be a challenging surgery in these patients, and the literature indicates that the best option is autologous reconstruction with costal cartilage. It is necessary to individualize each case to schedule nasal grafts and restructuring, and functional improvement in these cases is also essential.
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institution Kabale University
issn 1983-5175
2177-1235
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publishDate 2023-09-01
publisher Thieme Revinter Publicações Ltda.
record_format Article
series Revista Brasileira de Cirurgia Plástica
spelling doaj-art-a99b29a908b64bc482238063a3e041252025-08-20T03:57:00ZengThieme Revinter Publicações Ltda.Revista Brasileira de Cirurgia Plástica1983-51752177-12352023-09-0138310.5935/2177-1235.2023RBCP0786-ENNasal reconstruction using ribs in a patient with Binder syndrome: A case report and literature reviewOona Tomiê Daronch0Renata Fernanda Ramos Marcante1Laisa Brandão Carvalho2Aristides Augusto Palhares3Universidade Estadual Paulista, Botucatu, SP, BrazilUniversidade Estadual Paulista, Botucatu, SP, BrazilUniversidade Estadual Paulista, Botucatu, SP, BrazilUniversidade Estadual Paulista, Botucatu, SP, BrazilIntroduction: Binder’s syndrome can also be known as maxillonasal dysplasia and it is a congenital malformation characterized by nasomaxillary hypoplasia resulting from an underdevelopment of the middle facial skeleton. The current incidence or prevalence is still unknown, but it affects approximately one child in every 10,000 births. The diagnosis can be clinical or associated with prenatal ultrasonography, characterized by a flattened nose and abnormal maxillary convexity. The treatment is surgical to correct aesthetic and functional abnormalities. Case Report: Patient diagnosed with Binder’s syndrome at the age of 14, without other associated malformations, with aesthetic and functional nasal complaints. Surgical correction began with the extraction of a block of the sixth costal cartilage on the left, with a nasal opening on the columellar margin, in the pattern of an open rhinoplasty, and tissue dissection in the sub-SMAS plane. After preparing the nasal receptor area, a block of cartilage was sculpted for reconstruction of the nasal dorsum, alar grafts and septal cartilage grafts. There was an improvement in the projection of the nasal tip and nasal dorsum. Conclusion: Rhinoplasty can be a challenging surgery in these patients, and the literature indicates that the best option is autologous reconstruction with costal cartilage. It is necessary to individualize each case to schedule nasal grafts and restructuring, and functional improvement in these cases is also essential.http://www.rbcp.org.br/export-pdf/3358/1983-5175-rbcp-38-03-e0786-en.pdfcraniofacial dysostosisreconstructive surgical proceduresnosecartilagecostal cartilage
spellingShingle Oona Tomiê Daronch
Renata Fernanda Ramos Marcante
Laisa Brandão Carvalho
Aristides Augusto Palhares
Nasal reconstruction using ribs in a patient with Binder syndrome: A case report and literature review
Revista Brasileira de Cirurgia Plástica
craniofacial dysostosis
reconstructive surgical procedures
nose
cartilage
costal cartilage
title Nasal reconstruction using ribs in a patient with Binder syndrome: A case report and literature review
title_full Nasal reconstruction using ribs in a patient with Binder syndrome: A case report and literature review
title_fullStr Nasal reconstruction using ribs in a patient with Binder syndrome: A case report and literature review
title_full_unstemmed Nasal reconstruction using ribs in a patient with Binder syndrome: A case report and literature review
title_short Nasal reconstruction using ribs in a patient with Binder syndrome: A case report and literature review
title_sort nasal reconstruction using ribs in a patient with binder syndrome a case report and literature review
topic craniofacial dysostosis
reconstructive surgical procedures
nose
cartilage
costal cartilage
url http://www.rbcp.org.br/export-pdf/3358/1983-5175-rbcp-38-03-e0786-en.pdf
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AT renatafernandaramosmarcante nasalreconstructionusingribsinapatientwithbindersyndromeacasereportandliteraturereview
AT laisabrandaocarvalho nasalreconstructionusingribsinapatientwithbindersyndromeacasereportandliteraturereview
AT aristidesaugustopalhares nasalreconstructionusingribsinapatientwithbindersyndromeacasereportandliteraturereview