Marfan Syndrome: A Case Report

Marfan syndrome is an autosomal dominant systemic disorder of the connective tissue. Children affected by the Marfan syndrome carry a mutation in one of their two copies of the gene that encodes the connective tissue protein fibrillin-1. Marfan syndrome affects most organs and tissues, especially th...

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Bibliographic Details
Main Authors: Rajendran Ganesh, Rajendran Vijayakumar, Haridoss Selvakumar
Format: Article
Language:English
Published: Wiley 2012-01-01
Series:Case Reports in Dentistry
Online Access:http://dx.doi.org/10.1155/2012/595343
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Summary:Marfan syndrome is an autosomal dominant systemic disorder of the connective tissue. Children affected by the Marfan syndrome carry a mutation in one of their two copies of the gene that encodes the connective tissue protein fibrillin-1. Marfan syndrome affects most organs and tissues, especially the skeleton, lungs, eyes, heart, and the large blood vessel that distributes blood from the heart to the rest of the body. A case report of Marfan syndrome has been reported with oral features. The dental problems of the child were treated under general anesthesia and a one-month review showed intact stainless steel crowns' restorations and no signs of secondary caries.
ISSN:2090-6447
2090-6455