IgG4-related Disease Manifesting as Autoimmune Pancreatitis, Sialadenitis, and Cholangitis: Case Report
IgG4-related disease (IgG4-RD) is a rare autoimmune disease which can affect almost any organ. We present a case of IgG4-RD, which manifested as chronic autoimmune pancreatitis with pancreatic insufficiency, severe malnutrition, autoimmune sialadenitis, and cholangitis. After the administration of...
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| Format: | Article |
| Language: | English |
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Vilnius University Press
2025-08-01
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| Series: | Acta Medica Lituanica |
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| Online Access: | https://www.journals.vu.lt/AML/article/view/40864 |
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| _version_ | 1849223304621064192 |
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| author | Augustina Tumelytė Vytautas Rimkus Paulina Tekoriutė Limas Kupčinskas |
| author_facet | Augustina Tumelytė Vytautas Rimkus Paulina Tekoriutė Limas Kupčinskas |
| author_sort | Augustina Tumelytė |
| collection | DOAJ |
| description |
IgG4-related disease (IgG4-RD) is a rare autoimmune disease which can affect almost any organ. We present a case of IgG4-RD, which manifested as chronic autoimmune pancreatitis with pancreatic insufficiency, severe malnutrition, autoimmune sialadenitis, and cholangitis. After the administration of prednisolone and mycophenolate mofetil, the patient’s condition improved significantly.
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| format | Article |
| id | doaj-art-98f439406a3a47a390f86a00b78f4ac8 |
| institution | Kabale University |
| issn | 1392-0138 2029-4174 |
| language | English |
| publishDate | 2025-08-01 |
| publisher | Vilnius University Press |
| record_format | Article |
| series | Acta Medica Lituanica |
| spelling | doaj-art-98f439406a3a47a390f86a00b78f4ac82025-08-25T18:14:07ZengVilnius University PressActa Medica Lituanica1392-01382029-41742025-08-0132210.15388/Amed.2025.32.2.11IgG4-related Disease Manifesting as Autoimmune Pancreatitis, Sialadenitis, and Cholangitis: Case ReportAugustina Tumelytė0Vytautas Rimkus1https://orcid.org/0009-0006-5481-0721Paulina Tekoriutė2Limas Kupčinskas3https://orcid.org/0000-0002-8689-9023Lithuanian University of Health SciencesLithuanian University of Health SciencesLithuanian University of Health SciencesLithuanian University of Health Sciences IgG4-related disease (IgG4-RD) is a rare autoimmune disease which can affect almost any organ. We present a case of IgG4-RD, which manifested as chronic autoimmune pancreatitis with pancreatic insufficiency, severe malnutrition, autoimmune sialadenitis, and cholangitis. After the administration of prednisolone and mycophenolate mofetil, the patient’s condition improved significantly. https://www.journals.vu.lt/AML/article/view/40864IgG4-related diseaseautoimmune pancreatitissialadenitischolangitis |
| spellingShingle | Augustina Tumelytė Vytautas Rimkus Paulina Tekoriutė Limas Kupčinskas IgG4-related Disease Manifesting as Autoimmune Pancreatitis, Sialadenitis, and Cholangitis: Case Report Acta Medica Lituanica IgG4-related disease autoimmune pancreatitis sialadenitis cholangitis |
| title | IgG4-related Disease Manifesting as Autoimmune Pancreatitis, Sialadenitis, and Cholangitis: Case Report |
| title_full | IgG4-related Disease Manifesting as Autoimmune Pancreatitis, Sialadenitis, and Cholangitis: Case Report |
| title_fullStr | IgG4-related Disease Manifesting as Autoimmune Pancreatitis, Sialadenitis, and Cholangitis: Case Report |
| title_full_unstemmed | IgG4-related Disease Manifesting as Autoimmune Pancreatitis, Sialadenitis, and Cholangitis: Case Report |
| title_short | IgG4-related Disease Manifesting as Autoimmune Pancreatitis, Sialadenitis, and Cholangitis: Case Report |
| title_sort | igg4 related disease manifesting as autoimmune pancreatitis sialadenitis and cholangitis case report |
| topic | IgG4-related disease autoimmune pancreatitis sialadenitis cholangitis |
| url | https://www.journals.vu.lt/AML/article/view/40864 |
| work_keys_str_mv | AT augustinatumelyte igg4relateddiseasemanifestingasautoimmunepancreatitissialadenitisandcholangitiscasereport AT vytautasrimkus igg4relateddiseasemanifestingasautoimmunepancreatitissialadenitisandcholangitiscasereport AT paulinatekoriute igg4relateddiseasemanifestingasautoimmunepancreatitissialadenitisandcholangitiscasereport AT limaskupcinskas igg4relateddiseasemanifestingasautoimmunepancreatitissialadenitisandcholangitiscasereport |