JAKi for Dermatomyositis

Dermatomyositis (DM) is a systemic autoimmune rheumatic disease which can affect multi-organs, such as skin, muscle and lung. Five myositis-specific autoantibodies, i.e., TIF1r, MDA5, NXP2, Mi2 and SAE, are sero-markers of diagnostic value. The treatments for DM included glucocorticoids, csDMARDs, I...

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Main Author: Shuang Ye
Format: Article
Language:English
Published: World Scientific Publishing 2024-01-01
Series:Journal of Clinical Rheumatology and Immunology
Online Access:https://www.worldscientific.com/doi/10.1142/S266134172474016X
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author Shuang Ye
author_facet Shuang Ye
author_sort Shuang Ye
collection DOAJ
description Dermatomyositis (DM) is a systemic autoimmune rheumatic disease which can affect multi-organs, such as skin, muscle and lung. Five myositis-specific autoantibodies, i.e., TIF1r, MDA5, NXP2, Mi2 and SAE, are sero-markers of diagnostic value. The treatments for DM included glucocorticoids, csDMARDs, IVIg and biologics, e.g., rituximab. Type I IFN pathway is considered to be crucial in the pathogenesis of DM and the evidence of JAK inhibitors as treatment option in DM is accumulating. Herein, four clinical scenarios of DM, i.e., MDA5+DM-ILD, TIF1r+ cancer-associated DM, NXP2+ adult DM with GI involvement, and MSA negative DM, are presented to reveal the trials and tribulations to tackle this very difficult disease.
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issn 2661-3417
2661-3425
language English
publishDate 2024-01-01
publisher World Scientific Publishing
record_format Article
series Journal of Clinical Rheumatology and Immunology
spelling doaj-art-97c9ea0da41d44fd87ba14648fd2a75f2024-11-12T08:27:23ZengWorld Scientific PublishingJournal of Clinical Rheumatology and Immunology2661-34172661-34252024-01-0124supp01161610.1142/S266134172474016XJAKi for DermatomyositisShuang Ye0ChinaDermatomyositis (DM) is a systemic autoimmune rheumatic disease which can affect multi-organs, such as skin, muscle and lung. Five myositis-specific autoantibodies, i.e., TIF1r, MDA5, NXP2, Mi2 and SAE, are sero-markers of diagnostic value. The treatments for DM included glucocorticoids, csDMARDs, IVIg and biologics, e.g., rituximab. Type I IFN pathway is considered to be crucial in the pathogenesis of DM and the evidence of JAK inhibitors as treatment option in DM is accumulating. Herein, four clinical scenarios of DM, i.e., MDA5+DM-ILD, TIF1r+ cancer-associated DM, NXP2+ adult DM with GI involvement, and MSA negative DM, are presented to reveal the trials and tribulations to tackle this very difficult disease.https://www.worldscientific.com/doi/10.1142/S266134172474016X
spellingShingle Shuang Ye
JAKi for Dermatomyositis
Journal of Clinical Rheumatology and Immunology
title JAKi for Dermatomyositis
title_full JAKi for Dermatomyositis
title_fullStr JAKi for Dermatomyositis
title_full_unstemmed JAKi for Dermatomyositis
title_short JAKi for Dermatomyositis
title_sort jaki for dermatomyositis
url https://www.worldscientific.com/doi/10.1142/S266134172474016X
work_keys_str_mv AT shuangye jakifordermatomyositis