Sarcoidosis: Pathogenesis, Diagnosis, and Clinical Management

Introduction: Sarcoidosis is a multisystem inflammatory disease of unknown etiology. It is more common in women and in people suffering from obesity.  A characteristic feature is the formation of non-sarcomatous granulomas, which could occure important organs. It could also present as an asymptomat...

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Main Authors: Marcin Kuliga, Mateusz Bajak, Dominik Maciej Feret, Jadwiga Inglot, Julia Inglot, Maciej Mamczur, Julia Słowik, Damian Sowa, Michał Szczepański, Daniel Zapasek
Format: Article
Language:English
Published: Nicolaus Copernicus University in Toruń 2024-12-01
Series:Quality in Sport
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Online Access:https://apcz.umk.pl/QS/article/view/56213
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author Marcin Kuliga
Mateusz Bajak
Dominik Maciej Feret
Jadwiga Inglot
Julia Inglot
Maciej Mamczur
Julia Słowik
Damian Sowa
Michał Szczepański
Daniel Zapasek
author_facet Marcin Kuliga
Mateusz Bajak
Dominik Maciej Feret
Jadwiga Inglot
Julia Inglot
Maciej Mamczur
Julia Słowik
Damian Sowa
Michał Szczepański
Daniel Zapasek
author_sort Marcin Kuliga
collection DOAJ
description Introduction: Sarcoidosis is a multisystem inflammatory disease of unknown etiology. It is more common in women and in people suffering from obesity.  A characteristic feature is the formation of non-sarcomatous granulomas, which could occure important organs. It could also present as an asymptomatic form, and its diagnosis may be made incidentally on a routine chest X-ray. Aim of the study:   The aim of this study was to review the literature describing the disease sarcoidosis-its course, clinical forms, diagnosis and treatment. Methods and materials: : We reviewed the literature available in the PubMed database, using the key words: "sarcoidosis"; "granulomatosis’’; “cardiac sarcoidosis”; “neurosarcoidosis”; "pulmonary sarcoidosis''. Results: The most common form of sarcoidosis is pulmonary, with enlargement of hilar lymph nodes and parenchymal lesions. The disease could manifest itself in the form of skin lesions-specifically and non-specifically, ocular lesions, where nay most often appears as uveitis, usually bilateral, and could also involve the heart. Patients with neurosarcoidosis usually have involvement of the pituitary, hypothalamus, meninges and cranial nerves. Conclusion: The diagnosis of sarcoidosis is difficult because its symptoms are often nonspecific. Diagnosis is based on exclusion of other diseases and is confirmed through imaging, histopathological, and immunological tests. In most cases, the prognosis of sarcoidosis is positive, and the disease may resolve spontaneously or under treatment. Treatment of sarcoidosis depends on the severity of the disease and the involvement of specific organs, the most common treatment is glucocorticoids.  
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issn 2450-3118
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publisher Nicolaus Copernicus University in Toruń
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spelling doaj-art-8f4a4fb3e9f04a6e9241caab697116262024-12-15T08:08:24ZengNicolaus Copernicus University in ToruńQuality in Sport2450-31182024-12-013510.12775/QS.2024.35.56213Sarcoidosis: Pathogenesis, Diagnosis, and Clinical ManagementMarcin Kuliga0Mateusz Bajak1Dominik Maciej Feret2Jadwiga Inglot3Julia Inglot4Maciej Mamczur5Julia Słowik6Damian Sowa7Michał Szczepański8Daniel Zapasek9University of Rzeszów, Tadeusza Rejtana 16c, 35-310 Rzeszów, PolandUniversity Teaching Hospital them F. Chopin in Rzeszów, Fryderyka Szopena 2, 35-055 Rzeszów, Poland Independent Public Health Care Complex No. 1 in Rzeszów, ul. Czackiego 3, 35-051 Rzeszów, Poland Clinical Provincial Hospital No. 2 in Rzeszów, Lwowska 60, 35-301 Rzeszów, Poland Clinical Provincial Hospital No. 2 in Rzeszow, Lwowska 60, 35-301 Rzeszów, PolandMedical Center in Łańcut, Ignacego Paderewskiego 5, 37-100 Łańcut, Poland University Teaching Hospital them F. Chopin in Rzeszów, Fryderyka Szopena 2, 35-055 Rzeszów, PolandClinical Provincial Hospital No. 2 in Rzeszow, Lwowska 60, 35-301 Rzeszów, PolandMedical Center in Łańcut, Ignacego Paderewskiego 5, 37-100 Łańcut, Poland Medical Center in Łańcut, Ignacego Paderewskiego 5, 37-100 Łańcut, Poland Introduction: Sarcoidosis is a multisystem inflammatory disease of unknown etiology. It is more common in women and in people suffering from obesity.  A characteristic feature is the formation of non-sarcomatous granulomas, which could occure important organs. It could also present as an asymptomatic form, and its diagnosis may be made incidentally on a routine chest X-ray. Aim of the study:   The aim of this study was to review the literature describing the disease sarcoidosis-its course, clinical forms, diagnosis and treatment. Methods and materials: : We reviewed the literature available in the PubMed database, using the key words: "sarcoidosis"; "granulomatosis’’; “cardiac sarcoidosis”; “neurosarcoidosis”; "pulmonary sarcoidosis''. Results: The most common form of sarcoidosis is pulmonary, with enlargement of hilar lymph nodes and parenchymal lesions. The disease could manifest itself in the form of skin lesions-specifically and non-specifically, ocular lesions, where nay most often appears as uveitis, usually bilateral, and could also involve the heart. Patients with neurosarcoidosis usually have involvement of the pituitary, hypothalamus, meninges and cranial nerves. Conclusion: The diagnosis of sarcoidosis is difficult because its symptoms are often nonspecific. Diagnosis is based on exclusion of other diseases and is confirmed through imaging, histopathological, and immunological tests. In most cases, the prognosis of sarcoidosis is positive, and the disease may resolve spontaneously or under treatment. Treatment of sarcoidosis depends on the severity of the disease and the involvement of specific organs, the most common treatment is glucocorticoids.   https://apcz.umk.pl/QS/article/view/56213SarkoidozaGranumatozaSarkoidza sercaNeurosarkoidozaSarkoida płuczna
spellingShingle Marcin Kuliga
Mateusz Bajak
Dominik Maciej Feret
Jadwiga Inglot
Julia Inglot
Maciej Mamczur
Julia Słowik
Damian Sowa
Michał Szczepański
Daniel Zapasek
Sarcoidosis: Pathogenesis, Diagnosis, and Clinical Management
Quality in Sport
Sarkoidoza
Granumatoza
Sarkoidza serca
Neurosarkoidoza
Sarkoida płuczna
title Sarcoidosis: Pathogenesis, Diagnosis, and Clinical Management
title_full Sarcoidosis: Pathogenesis, Diagnosis, and Clinical Management
title_fullStr Sarcoidosis: Pathogenesis, Diagnosis, and Clinical Management
title_full_unstemmed Sarcoidosis: Pathogenesis, Diagnosis, and Clinical Management
title_short Sarcoidosis: Pathogenesis, Diagnosis, and Clinical Management
title_sort sarcoidosis pathogenesis diagnosis and clinical management
topic Sarkoidoza
Granumatoza
Sarkoidza serca
Neurosarkoidoza
Sarkoida płuczna
url https://apcz.umk.pl/QS/article/view/56213
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AT mateuszbajak sarcoidosispathogenesisdiagnosisandclinicalmanagement
AT dominikmaciejferet sarcoidosispathogenesisdiagnosisandclinicalmanagement
AT jadwigainglot sarcoidosispathogenesisdiagnosisandclinicalmanagement
AT juliainglot sarcoidosispathogenesisdiagnosisandclinicalmanagement
AT maciejmamczur sarcoidosispathogenesisdiagnosisandclinicalmanagement
AT juliasłowik sarcoidosispathogenesisdiagnosisandclinicalmanagement
AT damiansowa sarcoidosispathogenesisdiagnosisandclinicalmanagement
AT michałszczepanski sarcoidosispathogenesisdiagnosisandclinicalmanagement
AT danielzapasek sarcoidosispathogenesisdiagnosisandclinicalmanagement