A case report of desmoplastic fibroma in a three-year-old black African girl
Background: Desmoplastic fibroma is a very rare bone tumour that is commonly recognised by its striking resemblance to desmoid fibromatosis, commonly seen in soft tissues. Case Presentation: A 3-year-old girl presented to the Oral and Maxillofacial Department with swelling on the lower jaw for 4...
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| Language: | English |
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Babcock Medical Society
2024-12-01
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| Series: | Babcock University Medical Journal |
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| Online Access: | http://bumj.babcock.edu.ng/index.php/bumj/article/view/408 |
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| author | Olaejirinde Olaofe Chigozie Okongwu Godwin Umerah Oluwatosin Omoyiola Omolade Betiku |
| author_facet | Olaejirinde Olaofe Chigozie Okongwu Godwin Umerah Oluwatosin Omoyiola Omolade Betiku |
| author_sort | Olaejirinde Olaofe |
| collection | DOAJ |
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Background: Desmoplastic fibroma is a very rare bone tumour that is commonly recognised by its striking resemblance to desmoid fibromatosis, commonly seen in soft tissues.
Case Presentation: A 3-year-old girl presented to the Oral and Maxillofacial Department with swelling on the lower jaw for 4 months duration. Extra-oral examination revealed: Facial asymmetry due to the discrete swelling on the right mandible measuring 14 x 12cm in widest diameter below the right pre-auricular region to the right mental region. The Craniofacial CT scan showed an expansile jaw mass with destruction of the mandible. There was no evidence of bone formation. Histopathology diagnosis was desmoplastic fibroma of the bone. The tumour cells were weakly positive for MyoD1.
Conclusion: Pathologists must know that cells of desmoplastic fibroma may sometimes be weakly positive for MyoD1, as in rhabdomyosarcoma.
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| format | Article |
| id | doaj-art-679bae0516884f668261e3b651d621f9 |
| institution | Kabale University |
| issn | 2465-6666 2756-4657 |
| language | English |
| publishDate | 2024-12-01 |
| publisher | Babcock Medical Society |
| record_format | Article |
| series | Babcock University Medical Journal |
| spelling | doaj-art-679bae0516884f668261e3b651d621f92025-01-05T18:31:38ZengBabcock Medical SocietyBabcock University Medical Journal2465-66662756-46572024-12-017210.38029/babcockuniv.med.j..v7i2.408A case report of desmoplastic fibroma in a three-year-old black African girlOlaejirinde Olaofe0Chigozie Okongwu1Godwin Umerah2Oluwatosin Omoyiola3Omolade Betiku4Department of Morbid Anatomy and Forensic Medicine, Faculty of Basic Medical Sciences, College of Health Sciences, Obafemi Awolowo University, Ile-Ife, Osun State, NigeriaDepartment of Morbid Anatomy and Forensic Medicine, Obafemi Awolowo University Teaching Hospitals Complex, Ile-Ife, Osun State, NigeriaDepartment of Morbid Anatomy and Forensic Medicine, Obafemi Awolowo University Teaching Hospitals Complex, Ile-Ife, Osun State, NigeriaDepartment of Morbid Anatomy and Forensic Medicine, Obafemi Awolowo University Teaching Hospitals Complex, Ile-Ife, Osun State, NigeriaDepartment of Morbid Anatomy and Forensic Medicine, Obafemi Awolowo University Teaching Hospitals Complex, Ile-Ife, Osun State, Nigeria Background: Desmoplastic fibroma is a very rare bone tumour that is commonly recognised by its striking resemblance to desmoid fibromatosis, commonly seen in soft tissues. Case Presentation: A 3-year-old girl presented to the Oral and Maxillofacial Department with swelling on the lower jaw for 4 months duration. Extra-oral examination revealed: Facial asymmetry due to the discrete swelling on the right mandible measuring 14 x 12cm in widest diameter below the right pre-auricular region to the right mental region. The Craniofacial CT scan showed an expansile jaw mass with destruction of the mandible. There was no evidence of bone formation. Histopathology diagnosis was desmoplastic fibroma of the bone. The tumour cells were weakly positive for MyoD1. Conclusion: Pathologists must know that cells of desmoplastic fibroma may sometimes be weakly positive for MyoD1, as in rhabdomyosarcoma. http://bumj.babcock.edu.ng/index.php/bumj/article/view/408Desmoplastic fibromaMandibleImmunohistochemistryBiopsySpindle cell |
| spellingShingle | Olaejirinde Olaofe Chigozie Okongwu Godwin Umerah Oluwatosin Omoyiola Omolade Betiku A case report of desmoplastic fibroma in a three-year-old black African girl Babcock University Medical Journal Desmoplastic fibroma Mandible Immunohistochemistry Biopsy Spindle cell |
| title | A case report of desmoplastic fibroma in a three-year-old black African girl |
| title_full | A case report of desmoplastic fibroma in a three-year-old black African girl |
| title_fullStr | A case report of desmoplastic fibroma in a three-year-old black African girl |
| title_full_unstemmed | A case report of desmoplastic fibroma in a three-year-old black African girl |
| title_short | A case report of desmoplastic fibroma in a three-year-old black African girl |
| title_sort | case report of desmoplastic fibroma in a three year old black african girl |
| topic | Desmoplastic fibroma Mandible Immunohistochemistry Biopsy Spindle cell |
| url | http://bumj.babcock.edu.ng/index.php/bumj/article/view/408 |
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