Renal PEComa in a young male: A case report and insights from the literature
Perivascular epithelioid cell tumors (PEComas) are rare mesenchymal neoplasms, commonly found in the uterus and retroperitoneum. Renal PEComas are exceedingly rare, often posing diagnostic challenges due to their resemblance to renal cell carcinoma (RCC) on imaging. We present the case of an 18-year...
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Elsevier
2025-01-01
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Series: | Urology Case Reports |
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Online Access: | http://www.sciencedirect.com/science/article/pii/S2214442024002444 |
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author | Rashad Sholan Rufat Aliyev Malahat Sultan Anar Almazkhanli Savalan Karim Jalal Gasimov |
author_facet | Rashad Sholan Rufat Aliyev Malahat Sultan Anar Almazkhanli Savalan Karim Jalal Gasimov |
author_sort | Rashad Sholan |
collection | DOAJ |
description | Perivascular epithelioid cell tumors (PEComas) are rare mesenchymal neoplasms, commonly found in the uterus and retroperitoneum. Renal PEComas are exceedingly rare, often posing diagnostic challenges due to their resemblance to renal cell carcinoma (RCC) on imaging. We present the case of an 18-year-old male who presented with non-specific symptoms of fever, chills, and shivering. Imaging revealed a renal mass, initially suspected to be RCC. However, following a right radical nephrectomy, histopathological examination confirmed the diagnosis of malignant PEComa. This case highlights the rarity of renal PEComa and underscores the importance of early diagnosis and appropriate surgical management to prevent complications. |
format | Article |
id | doaj-art-6777bff207414f4284e9125e6ce18222 |
institution | Kabale University |
issn | 2214-4420 |
language | English |
publishDate | 2025-01-01 |
publisher | Elsevier |
record_format | Article |
series | Urology Case Reports |
spelling | doaj-art-6777bff207414f4284e9125e6ce182222025-01-14T04:12:16ZengElsevierUrology Case Reports2214-44202025-01-0158102890Renal PEComa in a young male: A case report and insights from the literatureRashad Sholan0Rufat Aliyev1Malahat Sultan2Anar Almazkhanli3Savalan Karim4Jalal Gasimov5Scientific Research Center, State Security Service Military Hospital, Baku, Azerbaijan; Corresponding author. AZ1000, Baku city, Badamdar, Mektebli street, 1, Azerbaijan.Scientific Research Center, State Security Service Military Hospital, Baku, AzerbaijanDepartment of Radiology, Azerbaijan Medical University, Baku, AzerbaijanDepartment of Kidney Diseases and Organ Transplantation, State Security Service Military Hospital, Baku, AzerbaijanDepartment of Pathology, State Security Service Military Hospital, Baku, AzerbaijanDepartment of the Emergency Medicine, State Security Service Military Hospital, Baku, AzerbaijanPerivascular epithelioid cell tumors (PEComas) are rare mesenchymal neoplasms, commonly found in the uterus and retroperitoneum. Renal PEComas are exceedingly rare, often posing diagnostic challenges due to their resemblance to renal cell carcinoma (RCC) on imaging. We present the case of an 18-year-old male who presented with non-specific symptoms of fever, chills, and shivering. Imaging revealed a renal mass, initially suspected to be RCC. However, following a right radical nephrectomy, histopathological examination confirmed the diagnosis of malignant PEComa. This case highlights the rarity of renal PEComa and underscores the importance of early diagnosis and appropriate surgical management to prevent complications.http://www.sciencedirect.com/science/article/pii/S2214442024002444PEComaRenal angiomyolipomaRenal cell carcinomaNephrectomy |
spellingShingle | Rashad Sholan Rufat Aliyev Malahat Sultan Anar Almazkhanli Savalan Karim Jalal Gasimov Renal PEComa in a young male: A case report and insights from the literature Urology Case Reports PEComa Renal angiomyolipoma Renal cell carcinoma Nephrectomy |
title | Renal PEComa in a young male: A case report and insights from the literature |
title_full | Renal PEComa in a young male: A case report and insights from the literature |
title_fullStr | Renal PEComa in a young male: A case report and insights from the literature |
title_full_unstemmed | Renal PEComa in a young male: A case report and insights from the literature |
title_short | Renal PEComa in a young male: A case report and insights from the literature |
title_sort | renal pecoma in a young male a case report and insights from the literature |
topic | PEComa Renal angiomyolipoma Renal cell carcinoma Nephrectomy |
url | http://www.sciencedirect.com/science/article/pii/S2214442024002444 |
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