Renal PEComa in a young male: A case report and insights from the literature

Perivascular epithelioid cell tumors (PEComas) are rare mesenchymal neoplasms, commonly found in the uterus and retroperitoneum. Renal PEComas are exceedingly rare, often posing diagnostic challenges due to their resemblance to renal cell carcinoma (RCC) on imaging. We present the case of an 18-year...

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Main Authors: Rashad Sholan, Rufat Aliyev, Malahat Sultan, Anar Almazkhanli, Savalan Karim, Jalal Gasimov
Format: Article
Language:English
Published: Elsevier 2025-01-01
Series:Urology Case Reports
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Online Access:http://www.sciencedirect.com/science/article/pii/S2214442024002444
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author Rashad Sholan
Rufat Aliyev
Malahat Sultan
Anar Almazkhanli
Savalan Karim
Jalal Gasimov
author_facet Rashad Sholan
Rufat Aliyev
Malahat Sultan
Anar Almazkhanli
Savalan Karim
Jalal Gasimov
author_sort Rashad Sholan
collection DOAJ
description Perivascular epithelioid cell tumors (PEComas) are rare mesenchymal neoplasms, commonly found in the uterus and retroperitoneum. Renal PEComas are exceedingly rare, often posing diagnostic challenges due to their resemblance to renal cell carcinoma (RCC) on imaging. We present the case of an 18-year-old male who presented with non-specific symptoms of fever, chills, and shivering. Imaging revealed a renal mass, initially suspected to be RCC. However, following a right radical nephrectomy, histopathological examination confirmed the diagnosis of malignant PEComa. This case highlights the rarity of renal PEComa and underscores the importance of early diagnosis and appropriate surgical management to prevent complications.
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institution Kabale University
issn 2214-4420
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publishDate 2025-01-01
publisher Elsevier
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series Urology Case Reports
spelling doaj-art-6777bff207414f4284e9125e6ce182222025-01-14T04:12:16ZengElsevierUrology Case Reports2214-44202025-01-0158102890Renal PEComa in a young male: A case report and insights from the literatureRashad Sholan0Rufat Aliyev1Malahat Sultan2Anar Almazkhanli3Savalan Karim4Jalal Gasimov5Scientific Research Center, State Security Service Military Hospital, Baku, Azerbaijan; Corresponding author. AZ1000, Baku city, Badamdar, Mektebli street, 1, Azerbaijan.Scientific Research Center, State Security Service Military Hospital, Baku, AzerbaijanDepartment of Radiology, Azerbaijan Medical University, Baku, AzerbaijanDepartment of Kidney Diseases and Organ Transplantation, State Security Service Military Hospital, Baku, AzerbaijanDepartment of Pathology, State Security Service Military Hospital, Baku, AzerbaijanDepartment of the Emergency Medicine, State Security Service Military Hospital, Baku, AzerbaijanPerivascular epithelioid cell tumors (PEComas) are rare mesenchymal neoplasms, commonly found in the uterus and retroperitoneum. Renal PEComas are exceedingly rare, often posing diagnostic challenges due to their resemblance to renal cell carcinoma (RCC) on imaging. We present the case of an 18-year-old male who presented with non-specific symptoms of fever, chills, and shivering. Imaging revealed a renal mass, initially suspected to be RCC. However, following a right radical nephrectomy, histopathological examination confirmed the diagnosis of malignant PEComa. This case highlights the rarity of renal PEComa and underscores the importance of early diagnosis and appropriate surgical management to prevent complications.http://www.sciencedirect.com/science/article/pii/S2214442024002444PEComaRenal angiomyolipomaRenal cell carcinomaNephrectomy
spellingShingle Rashad Sholan
Rufat Aliyev
Malahat Sultan
Anar Almazkhanli
Savalan Karim
Jalal Gasimov
Renal PEComa in a young male: A case report and insights from the literature
Urology Case Reports
PEComa
Renal angiomyolipoma
Renal cell carcinoma
Nephrectomy
title Renal PEComa in a young male: A case report and insights from the literature
title_full Renal PEComa in a young male: A case report and insights from the literature
title_fullStr Renal PEComa in a young male: A case report and insights from the literature
title_full_unstemmed Renal PEComa in a young male: A case report and insights from the literature
title_short Renal PEComa in a young male: A case report and insights from the literature
title_sort renal pecoma in a young male a case report and insights from the literature
topic PEComa
Renal angiomyolipoma
Renal cell carcinoma
Nephrectomy
url http://www.sciencedirect.com/science/article/pii/S2214442024002444
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AT anaralmazkhanli renalpecomainayoungmaleacasereportandinsightsfromtheliterature
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