A Case of Right Ventricular Endomyocardial Fibrosis Presenting with Right Ventricular Failure in an Immunocompromised Patient

Endomyocardial fibrosis is a rare disease in India but an important cause of restrictive cardiomyopathy. A middle-aged nondiabetic nonhypertensive male presented to us with features of right heart failure. Echocardiography shows a grossly dilated right atrium, reduced right ventricular (RV) volume w...

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Main Authors: Ratul Ghosh, Biswajit Majumder, Shibsankar Sarkar, Somnath Maji
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2024-10-01
Series:Journal of Clinical and Preventive Cardiology
Subjects:
Online Access:https://journals.lww.com/10.4103/jcpc.jcpc_13_24
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author Ratul Ghosh
Biswajit Majumder
Shibsankar Sarkar
Somnath Maji
author_facet Ratul Ghosh
Biswajit Majumder
Shibsankar Sarkar
Somnath Maji
author_sort Ratul Ghosh
collection DOAJ
description Endomyocardial fibrosis is a rare disease in India but an important cause of restrictive cardiomyopathy. A middle-aged nondiabetic nonhypertensive male presented to us with features of right heart failure. Echocardiography shows a grossly dilated right atrium, reduced right ventricular (RV) volume with thickened RV wall, and obliteration of the apex of the right ventricle along with severe low-pressure tricuspid regurgitation. There was mild thickening and obliteration of left ventricular apex also. Cardiac magnetic resonance imaging was attempted but could not be done as the patient had severe claustrophobia. He was diagnosed as HIV positive and was started on ART. The patient was managed conservatively with loop diuretics along with ACE inhibitors and spironolactone, and is now doing well with regular follow-up.
format Article
id doaj-art-62e773e803fd47fd9d2321162fc192fe
institution Kabale University
issn 2250-3528
language English
publishDate 2024-10-01
publisher Wolters Kluwer Medknow Publications
record_format Article
series Journal of Clinical and Preventive Cardiology
spelling doaj-art-62e773e803fd47fd9d2321162fc192fe2025-01-10T12:19:01ZengWolters Kluwer Medknow PublicationsJournal of Clinical and Preventive Cardiology2250-35282024-10-01133717310.4103/jcpc.jcpc_13_24A Case of Right Ventricular Endomyocardial Fibrosis Presenting with Right Ventricular Failure in an Immunocompromised PatientRatul GhoshBiswajit MajumderShibsankar SarkarSomnath MajiEndomyocardial fibrosis is a rare disease in India but an important cause of restrictive cardiomyopathy. A middle-aged nondiabetic nonhypertensive male presented to us with features of right heart failure. Echocardiography shows a grossly dilated right atrium, reduced right ventricular (RV) volume with thickened RV wall, and obliteration of the apex of the right ventricle along with severe low-pressure tricuspid regurgitation. There was mild thickening and obliteration of left ventricular apex also. Cardiac magnetic resonance imaging was attempted but could not be done as the patient had severe claustrophobia. He was diagnosed as HIV positive and was started on ART. The patient was managed conservatively with loop diuretics along with ACE inhibitors and spironolactone, and is now doing well with regular follow-up.https://journals.lww.com/10.4103/jcpc.jcpc_13_24endomyocardial fibrosisright-sided endomyocardial fibrosisright heart failure
spellingShingle Ratul Ghosh
Biswajit Majumder
Shibsankar Sarkar
Somnath Maji
A Case of Right Ventricular Endomyocardial Fibrosis Presenting with Right Ventricular Failure in an Immunocompromised Patient
Journal of Clinical and Preventive Cardiology
endomyocardial fibrosis
right-sided endomyocardial fibrosis
right heart failure
title A Case of Right Ventricular Endomyocardial Fibrosis Presenting with Right Ventricular Failure in an Immunocompromised Patient
title_full A Case of Right Ventricular Endomyocardial Fibrosis Presenting with Right Ventricular Failure in an Immunocompromised Patient
title_fullStr A Case of Right Ventricular Endomyocardial Fibrosis Presenting with Right Ventricular Failure in an Immunocompromised Patient
title_full_unstemmed A Case of Right Ventricular Endomyocardial Fibrosis Presenting with Right Ventricular Failure in an Immunocompromised Patient
title_short A Case of Right Ventricular Endomyocardial Fibrosis Presenting with Right Ventricular Failure in an Immunocompromised Patient
title_sort case of right ventricular endomyocardial fibrosis presenting with right ventricular failure in an immunocompromised patient
topic endomyocardial fibrosis
right-sided endomyocardial fibrosis
right heart failure
url https://journals.lww.com/10.4103/jcpc.jcpc_13_24
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