Acute Bilateral Retrobulbar Optic Neuritis Revealing Sphenoethmoidal Sinus Neuroendocrine Carcinoma

Primary sinonasal neuroendocrine carcinoma is a rare tumor of extreme malignancy. The diagnosis is often made at an advanced stage. The most recently documented treatment for nonmetastatic paranasal sinus neuroendocrine carcinoma consists of chemotherapy (cisplatin-VP16) followed by radiotherapy. Su...

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Main Authors: Belfaiza Soukaina, Marion Chatain, Benjelloul Fatiha
Format: Article
Language:English
Published: Wolters Kluwer Medknow Publications 2023-01-01
Series:Indian Journal of Medical Specialities
Subjects:
Online Access:https://journals.lww.com/10.4103/injms.injms_130_22
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author Belfaiza Soukaina
Marion Chatain
Benjelloul Fatiha
author_facet Belfaiza Soukaina
Marion Chatain
Benjelloul Fatiha
author_sort Belfaiza Soukaina
collection DOAJ
description Primary sinonasal neuroendocrine carcinoma is a rare tumor of extreme malignancy. The diagnosis is often made at an advanced stage. The most recently documented treatment for nonmetastatic paranasal sinus neuroendocrine carcinoma consists of chemotherapy (cisplatin-VP16) followed by radiotherapy. Surgery is reserved for resectable tumors that do not respond well to chemotherapy. We report the case of a patient admitted for acute bilateral Retrobulbular optic neuropathy (RBON) revealing a sphenoethmoidal sinus neuroendocrine carcinoma.
format Article
id doaj-art-5dba7a3e02d344b094145d6ec06627e5
institution Kabale University
issn 0976-2884
0976-2892
language English
publishDate 2023-01-01
publisher Wolters Kluwer Medknow Publications
record_format Article
series Indian Journal of Medical Specialities
spelling doaj-art-5dba7a3e02d344b094145d6ec06627e52025-08-25T08:43:30ZengWolters Kluwer Medknow PublicationsIndian Journal of Medical Specialities0976-28840976-28922023-01-01141606210.4103/injms.injms_130_22Acute Bilateral Retrobulbar Optic Neuritis Revealing Sphenoethmoidal Sinus Neuroendocrine CarcinomaBelfaiza SoukainaMarion ChatainBenjelloul FatihaPrimary sinonasal neuroendocrine carcinoma is a rare tumor of extreme malignancy. The diagnosis is often made at an advanced stage. The most recently documented treatment for nonmetastatic paranasal sinus neuroendocrine carcinoma consists of chemotherapy (cisplatin-VP16) followed by radiotherapy. Surgery is reserved for resectable tumors that do not respond well to chemotherapy. We report the case of a patient admitted for acute bilateral Retrobulbular optic neuropathy (RBON) revealing a sphenoethmoidal sinus neuroendocrine carcinoma.https://journals.lww.com/10.4103/injms.injms_130_22acute bilateral retrobulbar optic neuritisradiotherapysphenoethmoidal sinus neuroendocrine
spellingShingle Belfaiza Soukaina
Marion Chatain
Benjelloul Fatiha
Acute Bilateral Retrobulbar Optic Neuritis Revealing Sphenoethmoidal Sinus Neuroendocrine Carcinoma
Indian Journal of Medical Specialities
acute bilateral retrobulbar optic neuritis
radiotherapy
sphenoethmoidal sinus neuroendocrine
title Acute Bilateral Retrobulbar Optic Neuritis Revealing Sphenoethmoidal Sinus Neuroendocrine Carcinoma
title_full Acute Bilateral Retrobulbar Optic Neuritis Revealing Sphenoethmoidal Sinus Neuroendocrine Carcinoma
title_fullStr Acute Bilateral Retrobulbar Optic Neuritis Revealing Sphenoethmoidal Sinus Neuroendocrine Carcinoma
title_full_unstemmed Acute Bilateral Retrobulbar Optic Neuritis Revealing Sphenoethmoidal Sinus Neuroendocrine Carcinoma
title_short Acute Bilateral Retrobulbar Optic Neuritis Revealing Sphenoethmoidal Sinus Neuroendocrine Carcinoma
title_sort acute bilateral retrobulbar optic neuritis revealing sphenoethmoidal sinus neuroendocrine carcinoma
topic acute bilateral retrobulbar optic neuritis
radiotherapy
sphenoethmoidal sinus neuroendocrine
url https://journals.lww.com/10.4103/injms.injms_130_22
work_keys_str_mv AT belfaizasoukaina acutebilateralretrobulbaropticneuritisrevealingsphenoethmoidalsinusneuroendocrinecarcinoma
AT marionchatain acutebilateralretrobulbaropticneuritisrevealingsphenoethmoidalsinusneuroendocrinecarcinoma
AT benjelloulfatiha acutebilateralretrobulbaropticneuritisrevealingsphenoethmoidalsinusneuroendocrinecarcinoma