Hemangiomatosis of the spleen in a patient with Klippel-Trenaunay syndrome: A case report
Hemangiomatosis of the spleen is a benign vascular condition occurring as a manifestation of systemic angiomatosis. It is usually associated with Klippel-Trenaunay syndrome (KTS), which is a rare congenital malformation characterized by a triad of varicose veins, bony and soft tissue hypertrophy, an...
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| Format: | Article |
| Language: | English |
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Wolters Kluwer Medknow Publications
2024-12-01
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| Series: | Indian Journal of Pathology and Microbiology |
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| Online Access: | https://journals.lww.com/10.4103/ijpm.ijpm_897_22 |
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| author | Dhaneshwar Namdeorao Lanjewar Kinalee Prafullbhai Chothani Mitsu Vinay Vaishnav Gyaneshwar Rao |
| author_facet | Dhaneshwar Namdeorao Lanjewar Kinalee Prafullbhai Chothani Mitsu Vinay Vaishnav Gyaneshwar Rao |
| author_sort | Dhaneshwar Namdeorao Lanjewar |
| collection | DOAJ |
| description | Hemangiomatosis of the spleen is a benign vascular condition occurring as a manifestation of systemic angiomatosis. It is usually associated with Klippel-Trenaunay syndrome (KTS), which is a rare congenital malformation characterized by a triad of varicose veins, bony and soft tissue hypertrophy, and cutaneous and visceral hemangiomas and/or venous malformations. The association of splenic hemangiomatosis with KTS is less documented in the literature. In this report, we describe a 63-year-old female who presented with massive splenomegaly, the histopathology of which showed features of diffuse hemangiomatosis. Based on the histopathological diagnosis, a retrospective evaluation of the patient was carried out and she was diagnosed as KTS. To the best of our knowledge, this is the first report in the Indian literature describing splenic hemangiomatosis in a patient with KTS. |
| format | Article |
| id | doaj-art-47d88302b45b48d7a5520b4c01bd1c34 |
| institution | Kabale University |
| issn | 0377-4929 0974-5130 |
| language | English |
| publishDate | 2024-12-01 |
| publisher | Wolters Kluwer Medknow Publications |
| record_format | Article |
| series | Indian Journal of Pathology and Microbiology |
| spelling | doaj-art-47d88302b45b48d7a5520b4c01bd1c342025-01-10T10:27:20ZengWolters Kluwer Medknow PublicationsIndian Journal of Pathology and Microbiology0377-49290974-51302024-12-0167490090210.4103/ijpm.ijpm_897_22Hemangiomatosis of the spleen in a patient with Klippel-Trenaunay syndrome: A case reportDhaneshwar Namdeorao LanjewarKinalee Prafullbhai ChothaniMitsu Vinay VaishnavGyaneshwar RaoHemangiomatosis of the spleen is a benign vascular condition occurring as a manifestation of systemic angiomatosis. It is usually associated with Klippel-Trenaunay syndrome (KTS), which is a rare congenital malformation characterized by a triad of varicose veins, bony and soft tissue hypertrophy, and cutaneous and visceral hemangiomas and/or venous malformations. The association of splenic hemangiomatosis with KTS is less documented in the literature. In this report, we describe a 63-year-old female who presented with massive splenomegaly, the histopathology of which showed features of diffuse hemangiomatosis. Based on the histopathological diagnosis, a retrospective evaluation of the patient was carried out and she was diagnosed as KTS. To the best of our knowledge, this is the first report in the Indian literature describing splenic hemangiomatosis in a patient with KTS.https://journals.lww.com/10.4103/ijpm.ijpm_897_22hemangiomatosisklippel-trenaunay syndromespleen |
| spellingShingle | Dhaneshwar Namdeorao Lanjewar Kinalee Prafullbhai Chothani Mitsu Vinay Vaishnav Gyaneshwar Rao Hemangiomatosis of the spleen in a patient with Klippel-Trenaunay syndrome: A case report Indian Journal of Pathology and Microbiology hemangiomatosis klippel-trenaunay syndrome spleen |
| title | Hemangiomatosis of the spleen in a patient with Klippel-Trenaunay syndrome: A case report |
| title_full | Hemangiomatosis of the spleen in a patient with Klippel-Trenaunay syndrome: A case report |
| title_fullStr | Hemangiomatosis of the spleen in a patient with Klippel-Trenaunay syndrome: A case report |
| title_full_unstemmed | Hemangiomatosis of the spleen in a patient with Klippel-Trenaunay syndrome: A case report |
| title_short | Hemangiomatosis of the spleen in a patient with Klippel-Trenaunay syndrome: A case report |
| title_sort | hemangiomatosis of the spleen in a patient with klippel trenaunay syndrome a case report |
| topic | hemangiomatosis klippel-trenaunay syndrome spleen |
| url | https://journals.lww.com/10.4103/ijpm.ijpm_897_22 |
| work_keys_str_mv | AT dhaneshwarnamdeoraolanjewar hemangiomatosisofthespleeninapatientwithklippeltrenaunaysyndromeacasereport AT kinaleeprafullbhaichothani hemangiomatosisofthespleeninapatientwithklippeltrenaunaysyndromeacasereport AT mitsuvinayvaishnav hemangiomatosisofthespleeninapatientwithklippeltrenaunaysyndromeacasereport AT gyaneshwarrao hemangiomatosisofthespleeninapatientwithklippeltrenaunaysyndromeacasereport |