Rapid Response to Penpulimab Combined With Anlotinib and Chemotherapy in a Thoracic SMARCA4‐UT Without PD‐L1 Expression: A Case Report and Review of Literature

ABSTRACT SMARCA4‐deficient undifferentiated tumor (SMARCA4‐UT) in the chest is a high‐grade malignant tumor that grows rapidly and often carries a poor prognosis. Unfortunately, there are currently no effective treatment available until now. Here, we report a case of SMARCA4‐UT in a patient who show...

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Main Authors: Yuanhang Wang, Kelei Zhao, Jingjing Zhang, Xiaohan Yuan, Yanting Liu, Jinghang Zhang, Ping Lu, Min Zhang
Format: Article
Language:English
Published: Wiley 2024-12-01
Series:The Clinical Respiratory Journal
Subjects:
Online Access:https://doi.org/10.1111/crj.70036
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author Yuanhang Wang
Kelei Zhao
Jingjing Zhang
Xiaohan Yuan
Yanting Liu
Jinghang Zhang
Ping Lu
Min Zhang
author_facet Yuanhang Wang
Kelei Zhao
Jingjing Zhang
Xiaohan Yuan
Yanting Liu
Jinghang Zhang
Ping Lu
Min Zhang
author_sort Yuanhang Wang
collection DOAJ
description ABSTRACT SMARCA4‐deficient undifferentiated tumor (SMARCA4‐UT) in the chest is a high‐grade malignant tumor that grows rapidly and often carries a poor prognosis. Unfortunately, there are currently no effective treatment available until now. Here, we report a case of SMARCA4‐UT in a patient who showed a swift response to a combination treatment of penpulimab, anlotinib, and chemotherapy. A 55‐year‐old man was diagnosed with thoracic SMARCA4‐UT along with metastases to multiple lymph nodes, the pleura, and bones. Immunohistochemical (IHC) testing indicated the absence of PD‐L1 expression in tumor cells. He was given sintilimab and anlotinib as first line treatment. However, a follow‐up chest CT revealed progressive disease (PD) after the first cycle treatment. Subsequently, the second line regimen was modified to etoposide and cisplatin (EP) combined with anlotinib and penpulimab. The effectiveness evaluation revealed partial remission (PR) following two cycles of the second‐line regimen treatment. Notably, the patient's progress‐free survival (PFS) exceeds 7 months and the overall survival up to 12 months. Our case implies that a combination of chemotherapy, anlotinib, and penpulimab might offer a promising therapeutic approach for PD‐L1‐negative thoracic SMARCA4‐UT.
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institution Kabale University
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language English
publishDate 2024-12-01
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series The Clinical Respiratory Journal
spelling doaj-art-374f6ac93a0148e4ab83f4f5c6d91b222024-12-26T04:22:37ZengWileyThe Clinical Respiratory Journal1752-69811752-699X2024-12-011812n/an/a10.1111/crj.70036Rapid Response to Penpulimab Combined With Anlotinib and Chemotherapy in a Thoracic SMARCA4‐UT Without PD‐L1 Expression: A Case Report and Review of LiteratureYuanhang Wang0Kelei Zhao1Jingjing Zhang2Xiaohan Yuan3Yanting Liu4Jinghang Zhang5Ping Lu6Min Zhang7Department of Oncology The First Affiliated Hospital of Xinxiang Medical University Weihui ChinaDepartment of Oncology The First Affiliated Hospital of Xinxiang Medical University Weihui ChinaDepartment of Oncology The First Affiliated Hospital of Xinxiang Medical University Weihui ChinaDepartment of Oncology The First Affiliated Hospital of Xinxiang Medical University Weihui ChinaDepartment of Oncology The First Affiliated Hospital of Xinxiang Medical University Weihui ChinaDepartment of Pathology The First Affiliated Hospital of Xinxiang Medical University Weihui ChinaDepartment of Oncology The First Affiliated Hospital of Xinxiang Medical University Weihui ChinaDepartment of Oncology The First Affiliated Hospital of Xinxiang Medical University Weihui ChinaABSTRACT SMARCA4‐deficient undifferentiated tumor (SMARCA4‐UT) in the chest is a high‐grade malignant tumor that grows rapidly and often carries a poor prognosis. Unfortunately, there are currently no effective treatment available until now. Here, we report a case of SMARCA4‐UT in a patient who showed a swift response to a combination treatment of penpulimab, anlotinib, and chemotherapy. A 55‐year‐old man was diagnosed with thoracic SMARCA4‐UT along with metastases to multiple lymph nodes, the pleura, and bones. Immunohistochemical (IHC) testing indicated the absence of PD‐L1 expression in tumor cells. He was given sintilimab and anlotinib as first line treatment. However, a follow‐up chest CT revealed progressive disease (PD) after the first cycle treatment. Subsequently, the second line regimen was modified to etoposide and cisplatin (EP) combined with anlotinib and penpulimab. The effectiveness evaluation revealed partial remission (PR) following two cycles of the second‐line regimen treatment. Notably, the patient's progress‐free survival (PFS) exceeds 7 months and the overall survival up to 12 months. Our case implies that a combination of chemotherapy, anlotinib, and penpulimab might offer a promising therapeutic approach for PD‐L1‐negative thoracic SMARCA4‐UT.https://doi.org/10.1111/crj.70036anlotinibimmune checkpoint inhibitorsthoracic SMARCA4‐deficient undifferentiated tumor
spellingShingle Yuanhang Wang
Kelei Zhao
Jingjing Zhang
Xiaohan Yuan
Yanting Liu
Jinghang Zhang
Ping Lu
Min Zhang
Rapid Response to Penpulimab Combined With Anlotinib and Chemotherapy in a Thoracic SMARCA4‐UT Without PD‐L1 Expression: A Case Report and Review of Literature
The Clinical Respiratory Journal
anlotinib
immune checkpoint inhibitors
thoracic SMARCA4‐deficient undifferentiated tumor
title Rapid Response to Penpulimab Combined With Anlotinib and Chemotherapy in a Thoracic SMARCA4‐UT Without PD‐L1 Expression: A Case Report and Review of Literature
title_full Rapid Response to Penpulimab Combined With Anlotinib and Chemotherapy in a Thoracic SMARCA4‐UT Without PD‐L1 Expression: A Case Report and Review of Literature
title_fullStr Rapid Response to Penpulimab Combined With Anlotinib and Chemotherapy in a Thoracic SMARCA4‐UT Without PD‐L1 Expression: A Case Report and Review of Literature
title_full_unstemmed Rapid Response to Penpulimab Combined With Anlotinib and Chemotherapy in a Thoracic SMARCA4‐UT Without PD‐L1 Expression: A Case Report and Review of Literature
title_short Rapid Response to Penpulimab Combined With Anlotinib and Chemotherapy in a Thoracic SMARCA4‐UT Without PD‐L1 Expression: A Case Report and Review of Literature
title_sort rapid response to penpulimab combined with anlotinib and chemotherapy in a thoracic smarca4 ut without pd l1 expression a case report and review of literature
topic anlotinib
immune checkpoint inhibitors
thoracic SMARCA4‐deficient undifferentiated tumor
url https://doi.org/10.1111/crj.70036
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