Gamma heavy chain disease associated with T-cell large granular lymphocyte lymphoproliferative disorder: case report and literature review.
Heavy chain diseases are rare B-cell neoplasms consisting of the production of a monoclonal immunoglobulin composed of the only heavy chain without corresponding light chains. It is a rare adult disease that may involve several sites with a variable clinical course. It manifests itself on a large s...
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| Format: | Article |
| Language: | English |
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PAGEPress Publications
2023-01-01
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| Series: | Mediterranean Journal of Hematology and Infectious Diseases |
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| Online Access: | http://www.mjhid.org/index.php/mjhid/article/view/5165 |
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| author | Maria Laura Bisegna Maria Assunta Limongiello Stefano Fiori Maria Stefania De Propris Irene Della Starza Stefania Trasarti |
| author_facet | Maria Laura Bisegna Maria Assunta Limongiello Stefano Fiori Maria Stefania De Propris Irene Della Starza Stefania Trasarti |
| author_sort | Maria Laura Bisegna |
| collection | DOAJ |
| description |
Heavy chain diseases are rare B-cell neoplasms consisting of the production of a monoclonal immunoglobulin composed of the only heavy chain without corresponding light chains. It is a rare adult disease that may involve several sites with a variable clinical course. It manifests itself on a large spectrum from indolent to rapidly progressive. We present a case of heavy chain disease and concomitant T- cell large granular lymphoproliferative disorder, an association described in only six cases before.
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| format | Article |
| id | doaj-art-361a2b12915a41d693af2a7c040d6ac0 |
| institution | Kabale University |
| issn | 2035-3006 |
| language | English |
| publishDate | 2023-01-01 |
| publisher | PAGEPress Publications |
| record_format | Article |
| series | Mediterranean Journal of Hematology and Infectious Diseases |
| spelling | doaj-art-361a2b12915a41d693af2a7c040d6ac02025-01-02T16:59:03ZengPAGEPress PublicationsMediterranean Journal of Hematology and Infectious Diseases2035-30062023-01-0115110.4084/MJHID.2023.010Gamma heavy chain disease associated with T-cell large granular lymphocyte lymphoproliferative disorder: case report and literature review.Maria Laura Bisegna0Maria Assunta Limongiello1Stefano Fiori2Maria Stefania De Propris3Irene Della Starza4Stefania Trasarti51. Hematology, Department of Translational and Precision Medicine, Sapienza University, Rome, Italy. Dipartimento di Diagnostica per Immagini, Radioterapia Oncologica ed Ematologia, Fondazione Policlinico Universitario A. Gemelli IRCCS, Roma, Italy.Division of Hematopathology, IEO, European Institute of Oncology IRCCS, 20141 Milan, Italy.1. Hematology, Department of Translational and Precision Medicine, Sapienza University, Rome, Italy.Hematology, Department of Translational and Precision Medicine, Sapienza University, Rome, Italy.Hematology, Department of Translational and Precision Medicine, Sapienza University, Rome, Italy. Heavy chain diseases are rare B-cell neoplasms consisting of the production of a monoclonal immunoglobulin composed of the only heavy chain without corresponding light chains. It is a rare adult disease that may involve several sites with a variable clinical course. It manifests itself on a large spectrum from indolent to rapidly progressive. We present a case of heavy chain disease and concomitant T- cell large granular lymphoproliferative disorder, an association described in only six cases before. http://www.mjhid.org/index.php/mjhid/article/view/5165gamma heavy-chain diseaselymphoproliferative disordersplasma cellelectrophoresis |
| spellingShingle | Maria Laura Bisegna Maria Assunta Limongiello Stefano Fiori Maria Stefania De Propris Irene Della Starza Stefania Trasarti Gamma heavy chain disease associated with T-cell large granular lymphocyte lymphoproliferative disorder: case report and literature review. Mediterranean Journal of Hematology and Infectious Diseases gamma heavy-chain disease lymphoproliferative disorders plasma cell electrophoresis |
| title | Gamma heavy chain disease associated with T-cell large granular lymphocyte lymphoproliferative disorder: case report and literature review. |
| title_full | Gamma heavy chain disease associated with T-cell large granular lymphocyte lymphoproliferative disorder: case report and literature review. |
| title_fullStr | Gamma heavy chain disease associated with T-cell large granular lymphocyte lymphoproliferative disorder: case report and literature review. |
| title_full_unstemmed | Gamma heavy chain disease associated with T-cell large granular lymphocyte lymphoproliferative disorder: case report and literature review. |
| title_short | Gamma heavy chain disease associated with T-cell large granular lymphocyte lymphoproliferative disorder: case report and literature review. |
| title_sort | gamma heavy chain disease associated with t cell large granular lymphocyte lymphoproliferative disorder case report and literature review |
| topic | gamma heavy-chain disease lymphoproliferative disorders plasma cell electrophoresis |
| url | http://www.mjhid.org/index.php/mjhid/article/view/5165 |
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