Insights for Stratification of Risk in Brugada Syndrome

Brugada syndrome (BrS) is an inherited disease with an increased risk of sudden cardiac death (SCD). However, testing identifies genetic disorders in only 20–30% of patients analysed, indicating a gap in knowledge of its genetic aetiology. Diagnosis relies on ECG, and risk stratification in BrS pati...

Full description

Saved in:
Bibliographic Details
Main Authors: Daniel García Iglesias, José Rubín, Diego Pérez, César Morís, David Calvo
Format: Article
Language:English
Published: Radcliffe Medical Media 2019-01-01
Series:European Cardiology Review
Online Access:https://www.ecrjournal.com/articles/insights-stratification-risk-brugada-syndrome
Tags: Add Tag
No Tags, Be the first to tag this record!
_version_ 1846122520895291392
author Daniel García Iglesias
José Rubín
Diego Pérez
César Morís
David Calvo
author_facet Daniel García Iglesias
José Rubín
Diego Pérez
César Morís
David Calvo
author_sort Daniel García Iglesias
collection DOAJ
description Brugada syndrome (BrS) is an inherited disease with an increased risk of sudden cardiac death (SCD). However, testing identifies genetic disorders in only 20–30% of patients analysed, indicating a gap in knowledge of its genetic aetiology. Diagnosis relies on ECG, and risk stratification in BrS patients is challenging, primarily because of the complexity of the issue. As a result, clinicians fail to provide the appropriate strategy for SCD prevention for many patients. Several variables and interventions are being studied to improve diagnostics and maximise patient protection. In addition, the scientific community must increase efforts to provide patient care according to knowledge and research for improving stratification of risk. In this article, the authors summarise contemporary evidence on clinical variables and provide an overview of future directions in risk stratification and SCD prevention.
format Article
id doaj-art-2b1eb1f2f459426889a4d69d8f443822
institution Kabale University
issn 1758-3756
1758-3764
language English
publishDate 2019-01-01
publisher Radcliffe Medical Media
record_format Article
series European Cardiology Review
spelling doaj-art-2b1eb1f2f459426889a4d69d8f4438222024-12-14T16:01:10ZengRadcliffe Medical MediaEuropean Cardiology Review1758-37561758-37642019-01-01141454910.15420/ecr.2018.31.2Insights for Stratification of Risk in Brugada SyndromeDaniel García Iglesias0José Rubín1Diego Pérez2César Morís3David Calvo4Arrhythmia Unit, Cardiology Department, Hospital Universitario Central de Asturias, Oviedo, Spain; Instituto de Investigación Sanitaria del Principado de Asturias, Oviedo, SpainArrhythmia Unit, Cardiology Department, Hospital Universitario Central de Asturias, Oviedo, Spain; Instituto de Investigación Sanitaria del Principado de Asturias, Oviedo, SpainArrhythmia Unit, Cardiology Department, Hospital Universitario Central de Asturias, Oviedo, Spain; Instituto de Investigación Sanitaria del Principado de Asturias, Oviedo, SpainArrhythmia Unit, Cardiology Department, Hospital Universitario Central de Asturias, Oviedo, Spain; Instituto de Investigación Sanitaria del Principado de Asturias, Oviedo, SpainArrhythmia Unit, Cardiology Department, Hospital Universitario Central de Asturias, Oviedo, Spain; Instituto de Investigación Sanitaria del Principado de Asturias, Oviedo, SpainBrugada syndrome (BrS) is an inherited disease with an increased risk of sudden cardiac death (SCD). However, testing identifies genetic disorders in only 20–30% of patients analysed, indicating a gap in knowledge of its genetic aetiology. Diagnosis relies on ECG, and risk stratification in BrS patients is challenging, primarily because of the complexity of the issue. As a result, clinicians fail to provide the appropriate strategy for SCD prevention for many patients. Several variables and interventions are being studied to improve diagnostics and maximise patient protection. In addition, the scientific community must increase efforts to provide patient care according to knowledge and research for improving stratification of risk. In this article, the authors summarise contemporary evidence on clinical variables and provide an overview of future directions in risk stratification and SCD prevention.https://www.ecrjournal.com/articles/insights-stratification-risk-brugada-syndrome
spellingShingle Daniel García Iglesias
José Rubín
Diego Pérez
César Morís
David Calvo
Insights for Stratification of Risk in Brugada Syndrome
European Cardiology Review
title Insights for Stratification of Risk in Brugada Syndrome
title_full Insights for Stratification of Risk in Brugada Syndrome
title_fullStr Insights for Stratification of Risk in Brugada Syndrome
title_full_unstemmed Insights for Stratification of Risk in Brugada Syndrome
title_short Insights for Stratification of Risk in Brugada Syndrome
title_sort insights for stratification of risk in brugada syndrome
url https://www.ecrjournal.com/articles/insights-stratification-risk-brugada-syndrome
work_keys_str_mv AT danielgarciaiglesias insightsforstratificationofriskinbrugadasyndrome
AT joserubin insightsforstratificationofriskinbrugadasyndrome
AT diegoperez insightsforstratificationofriskinbrugadasyndrome
AT cesarmoris insightsforstratificationofriskinbrugadasyndrome
AT davidcalvo insightsforstratificationofriskinbrugadasyndrome