HLA Haplotype Association with Celiac Disease in Albanian Pediatric Patients from Kosovo

Genetic predisposition to celiac disease (CD) is strongly associated with the presence of HLA alleles in the individual genotype encoding HLA-DQ2 and/or HLA-DQ8 heterodimers. The main aim of this study was to analyze the HLA-A, -B, -DRB1, and -DQ allele and five-locus haplotype frequencies in 60 Alb...

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Main Authors: Atifete Ramosaj-Morina, Marija Burek Kamenaric, Mehmedali Azemi, Lidvana Spahiu, Zorana Grubic, Renata Zunec
Format: Article
Language:English
Published: Wiley 2019-01-01
Series:Gastroenterology Research and Practice
Online Access:http://dx.doi.org/10.1155/2019/7369014
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author Atifete Ramosaj-Morina
Marija Burek Kamenaric
Mehmedali Azemi
Lidvana Spahiu
Zorana Grubic
Renata Zunec
author_facet Atifete Ramosaj-Morina
Marija Burek Kamenaric
Mehmedali Azemi
Lidvana Spahiu
Zorana Grubic
Renata Zunec
author_sort Atifete Ramosaj-Morina
collection DOAJ
description Genetic predisposition to celiac disease (CD) is strongly associated with the presence of HLA alleles in the individual genotype encoding HLA-DQ2 and/or HLA-DQ8 heterodimers. The main aim of this study was to analyze the HLA-A, -B, -DRB1, and -DQ allele and five-locus haplotype frequencies in 60 Albanian pediatric CD patients and 124 non-CD children from Kosovo. The most prevalent haplotype in patients was the ancestral AH 8.1 haplotype present in 22.5% of the cases compared to 2.8% of the controls (P<0.0001). Additionally, two other haplotypes were also overrepresented in patients (HLA-A∗02~B∗50~DRB1∗07~DQA1∗02:01~DQB1∗02:02 and HLA-A∗68~B∗44~DRB1∗07~DQA1∗02:01~DQB1∗02:02). Analysis showed that 95.0% of CD patients and 43.3% of controls were carriers of HLA-DQ2 and/or HLA-DQ8 heterodimers. The most frequent CD-predisposing HLA-DQ haplotypes in patients were HLA-DQ2.5 (46.7%) and HLA-DQ2.2 (11.6%), while the most prevalent genotypes were HLA-DQ2.5/DQX (58.3%) and HLA-DQ2.5/DQ2.2 (20.0%). The frequency of the HLA-DQ8 heterodimer among CD patients (4.2%) compared to the control group (8.1%) was without statistical significance. The given data demonstrate differences in the distribution of HLA haplotypes among Albanian CD patients from Kosovo in comparison to other European and non-European populations, as well as provide additional population data to supplement the thus far undisputed importance of the role of HLA-DQ2 and HLA-DQ8 heterodimers in the development of CD.
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series Gastroenterology Research and Practice
spelling doaj-art-27b7af2dfadb47ea94824a991feff9af2025-08-20T03:54:41ZengWileyGastroenterology Research and Practice1687-61211687-630X2019-01-01201910.1155/2019/73690147369014HLA Haplotype Association with Celiac Disease in Albanian Pediatric Patients from KosovoAtifete Ramosaj-Morina0Marija Burek Kamenaric1Mehmedali Azemi2Lidvana Spahiu3Zorana Grubic4Renata Zunec5Pediatric Clinic, University Clinical Centre of Kosovo, Rrethi i Spitalit p.n., 10000 Prishtina, KosovoTissue Typing Centre, Clinical Department of Transfusion Medicine and Transplantation Biology, University Hospital Centre Zagreb, Kispaticeva 12, HR-10000 Zagreb, CroatiaPediatric Clinic, University Clinical Centre of Kosovo, Rrethi i Spitalit p.n., 10000 Prishtina, KosovoPediatric Clinic, University Clinical Centre of Kosovo, Rrethi i Spitalit p.n., 10000 Prishtina, KosovoTissue Typing Centre, Clinical Department of Transfusion Medicine and Transplantation Biology, University Hospital Centre Zagreb, Kispaticeva 12, HR-10000 Zagreb, CroatiaTissue Typing Centre, Clinical Department of Transfusion Medicine and Transplantation Biology, University Hospital Centre Zagreb, Kispaticeva 12, HR-10000 Zagreb, CroatiaGenetic predisposition to celiac disease (CD) is strongly associated with the presence of HLA alleles in the individual genotype encoding HLA-DQ2 and/or HLA-DQ8 heterodimers. The main aim of this study was to analyze the HLA-A, -B, -DRB1, and -DQ allele and five-locus haplotype frequencies in 60 Albanian pediatric CD patients and 124 non-CD children from Kosovo. The most prevalent haplotype in patients was the ancestral AH 8.1 haplotype present in 22.5% of the cases compared to 2.8% of the controls (P<0.0001). Additionally, two other haplotypes were also overrepresented in patients (HLA-A∗02~B∗50~DRB1∗07~DQA1∗02:01~DQB1∗02:02 and HLA-A∗68~B∗44~DRB1∗07~DQA1∗02:01~DQB1∗02:02). Analysis showed that 95.0% of CD patients and 43.3% of controls were carriers of HLA-DQ2 and/or HLA-DQ8 heterodimers. The most frequent CD-predisposing HLA-DQ haplotypes in patients were HLA-DQ2.5 (46.7%) and HLA-DQ2.2 (11.6%), while the most prevalent genotypes were HLA-DQ2.5/DQX (58.3%) and HLA-DQ2.5/DQ2.2 (20.0%). The frequency of the HLA-DQ8 heterodimer among CD patients (4.2%) compared to the control group (8.1%) was without statistical significance. The given data demonstrate differences in the distribution of HLA haplotypes among Albanian CD patients from Kosovo in comparison to other European and non-European populations, as well as provide additional population data to supplement the thus far undisputed importance of the role of HLA-DQ2 and HLA-DQ8 heterodimers in the development of CD.http://dx.doi.org/10.1155/2019/7369014
spellingShingle Atifete Ramosaj-Morina
Marija Burek Kamenaric
Mehmedali Azemi
Lidvana Spahiu
Zorana Grubic
Renata Zunec
HLA Haplotype Association with Celiac Disease in Albanian Pediatric Patients from Kosovo
Gastroenterology Research and Practice
title HLA Haplotype Association with Celiac Disease in Albanian Pediatric Patients from Kosovo
title_full HLA Haplotype Association with Celiac Disease in Albanian Pediatric Patients from Kosovo
title_fullStr HLA Haplotype Association with Celiac Disease in Albanian Pediatric Patients from Kosovo
title_full_unstemmed HLA Haplotype Association with Celiac Disease in Albanian Pediatric Patients from Kosovo
title_short HLA Haplotype Association with Celiac Disease in Albanian Pediatric Patients from Kosovo
title_sort hla haplotype association with celiac disease in albanian pediatric patients from kosovo
url http://dx.doi.org/10.1155/2019/7369014
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