FVIII peptides presented on HLA-DP and identification of an A3 domain peptide binding with high affinity to the commonly expressed HLA-DP4

The development of neutralizing antibodies (inhibitors) against coagulation factor VIII (FVIII) poses a major challenge in hemophilia A (HA) treatment. The formation of FVIII inhibitors is a CD4+ T-cell dependent mechanism which includes antigen presenting cells (APCs), B- and T-helper lymphocytes....

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Main Authors: Mariarosaria Miranda, Bjarke Endel Hansen, Batoul Wehbi, Valeria Porcheddu, Floris P.J. van Alphen, Paul Kaijen, Karin Fijnvandraat, Sebastien Lacroix-Desmazes, Maartje van den Biggelaar, Bernard Maillere, Jan Voorberg, EDUC8 Consortium
Format: Article
Language:English
Published: Ferrata Storti Foundation 2024-12-01
Series:Haematologica
Online Access:https://haematologica.org/article/view/11868
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author Mariarosaria Miranda
Bjarke Endel Hansen
Batoul Wehbi
Valeria Porcheddu
Floris P.J. van Alphen
Paul Kaijen
Karin Fijnvandraat
Sebastien Lacroix-Desmazes
Maartje van den Biggelaar
Bernard Maillere
Jan Voorberg
EDUC8 Consortium
author_facet Mariarosaria Miranda
Bjarke Endel Hansen
Batoul Wehbi
Valeria Porcheddu
Floris P.J. van Alphen
Paul Kaijen
Karin Fijnvandraat
Sebastien Lacroix-Desmazes
Maartje van den Biggelaar
Bernard Maillere
Jan Voorberg
EDUC8 Consortium
author_sort Mariarosaria Miranda
collection DOAJ
description The development of neutralizing antibodies (inhibitors) against coagulation factor VIII (FVIII) poses a major challenge in hemophilia A (HA) treatment. The formation of FVIII inhibitors is a CD4+ T-cell dependent mechanism which includes antigen presenting cells (APCs), B- and T-helper lymphocytes. APCs present FVIII derived peptides on major histocompatibility complex class II (MHC-II) to CD4+ Tcells. We previously established a mass spectrometry based approach to delineate the FVIII repertoire presented on HLA-DR and HLA-DQ. In this study, specific attention was directed towards the identification of FVIII peptides presented on HLA-DP. A data-set of naturally processed FVIII peptides was generated by incubating human FVIII with immature monocytes-derived dendritic cells (moDCs) from HLA-typed healthy donors. Using this method, we identified 176 to 1352 different HLA-DP presented peptides per donor, including 26 different FVIII derived peptides. The most frequently presented peptides derived from the A3, and C2 domains of FVIII. Comparison of the FVIII repertoire presented on HLA-DP with that presented on HLA-DR revealed considerable overlap but also suggested preferential presentation of specific peptides on either HLA-DR or HLA-DP. Fourteen FVIII peptides presented on HLA-DP were synthesized and evaluated for their binding ability to the commonly expressed HLA-DP4 molecule which is highly prevalent in the Caucasian population. Peptide binding studies showed that 7 of 14 peptides competed with a reference peptide to HLADP4. Interestingly, an A3 domain derived peptide bound with high affinity to HLA-DP4 positioning this peptide as a prime candidate for the development of novel peptide-based tolerogenic strategies for FVIII inhibitors.
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publishDate 2024-12-01
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series Haematologica
spelling doaj-art-1d3765a7344b47d59f82ebbd401adcb12024-12-12T19:43:09ZengFerrata Storti FoundationHaematologica0390-60781592-87212024-12-01999110.3324/haematol.2024.286204FVIII peptides presented on HLA-DP and identification of an A3 domain peptide binding with high affinity to the commonly expressed HLA-DP4Mariarosaria Miranda0Bjarke Endel Hansen1Batoul Wehbi2Valeria Porcheddu3Floris P.J. van Alphen4Paul Kaijen5Karin Fijnvandraat6Sebastien Lacroix-Desmazes7Maartje van den Biggelaar8Bernard Maillere9Jan Voorberg10EDUC8 Consortium11Department of Molecular Hematology, Sanquin Research and Landsteiner Laboratory, AmsterdamImmudex, Copenhagen, DenmarkUniversite Paris-Saclay, C EA, INRAE, Departement Medicaments et T echnologies pour la Sante, SIMoS, Gif-sur-Y vetteUniversite Paris-Saclay, C EA, INRAE, Departement Medicaments et T echnologies pour la Sante, SIMoS, Gif-sur-Y vetteDepartment of Molecular Hematology, Sanquin Research and Landsteiner Laboratory, AmsterdamDepartment of Molecular Hematology, Sanquin Research and Landsteiner Laboratory, AmsterdamDepartment of Molecular Hematology, Sanquin Research and Landsteiner Laboratory, Amsterdam, The Netherlands; Amsterdam University Medical Center location University of Amsterdam, Department of Pediatric Hematology, AmsterdamInstitut National de la Sante et de la Recherche Medicale, Centre de Recherche des Cordeliers, CNRS, Sorbonne Universite, Universite Paris Cite, ParisDepartment of Molecular Hematology, Sanquin Research and Landsteiner Laboratory, AmsterdamUniversite Paris-Saclay, CEA, INRAE, Departement Medicaments et Technologies pourla Sante, SIMoS, Gif-sur-Y vetteDepartment of Molecular Hematology, Sanquin Research and Landsteiner Laboratory, Amsterdam, The Netherlands; Department of Experimental V ascular Medicine, Amsterdam University Medical C enter, AmsterdamFlora Peyvandi, Christoph Koenigs, Johannes Oldenburg, Yvette van Kooyk, Bernard Maillère, Sebastien Lacroix-Desmazes, Jan Voorberg The development of neutralizing antibodies (inhibitors) against coagulation factor VIII (FVIII) poses a major challenge in hemophilia A (HA) treatment. The formation of FVIII inhibitors is a CD4+ T-cell dependent mechanism which includes antigen presenting cells (APCs), B- and T-helper lymphocytes. APCs present FVIII derived peptides on major histocompatibility complex class II (MHC-II) to CD4+ Tcells. We previously established a mass spectrometry based approach to delineate the FVIII repertoire presented on HLA-DR and HLA-DQ. In this study, specific attention was directed towards the identification of FVIII peptides presented on HLA-DP. A data-set of naturally processed FVIII peptides was generated by incubating human FVIII with immature monocytes-derived dendritic cells (moDCs) from HLA-typed healthy donors. Using this method, we identified 176 to 1352 different HLA-DP presented peptides per donor, including 26 different FVIII derived peptides. The most frequently presented peptides derived from the A3, and C2 domains of FVIII. Comparison of the FVIII repertoire presented on HLA-DP with that presented on HLA-DR revealed considerable overlap but also suggested preferential presentation of specific peptides on either HLA-DR or HLA-DP. Fourteen FVIII peptides presented on HLA-DP were synthesized and evaluated for their binding ability to the commonly expressed HLA-DP4 molecule which is highly prevalent in the Caucasian population. Peptide binding studies showed that 7 of 14 peptides competed with a reference peptide to HLADP4. Interestingly, an A3 domain derived peptide bound with high affinity to HLA-DP4 positioning this peptide as a prime candidate for the development of novel peptide-based tolerogenic strategies for FVIII inhibitors. https://haematologica.org/article/view/11868
spellingShingle Mariarosaria Miranda
Bjarke Endel Hansen
Batoul Wehbi
Valeria Porcheddu
Floris P.J. van Alphen
Paul Kaijen
Karin Fijnvandraat
Sebastien Lacroix-Desmazes
Maartje van den Biggelaar
Bernard Maillere
Jan Voorberg
EDUC8 Consortium
FVIII peptides presented on HLA-DP and identification of an A3 domain peptide binding with high affinity to the commonly expressed HLA-DP4
Haematologica
title FVIII peptides presented on HLA-DP and identification of an A3 domain peptide binding with high affinity to the commonly expressed HLA-DP4
title_full FVIII peptides presented on HLA-DP and identification of an A3 domain peptide binding with high affinity to the commonly expressed HLA-DP4
title_fullStr FVIII peptides presented on HLA-DP and identification of an A3 domain peptide binding with high affinity to the commonly expressed HLA-DP4
title_full_unstemmed FVIII peptides presented on HLA-DP and identification of an A3 domain peptide binding with high affinity to the commonly expressed HLA-DP4
title_short FVIII peptides presented on HLA-DP and identification of an A3 domain peptide binding with high affinity to the commonly expressed HLA-DP4
title_sort fviii peptides presented on hla dp and identification of an a3 domain peptide binding with high affinity to the commonly expressed hla dp4
url https://haematologica.org/article/view/11868
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