Neonatal Epidermolytic Ichthyosis Caused by a KRT10 Mutation (c.467G>A, p.Arg156His): A Case Report

ABSTRACT We present a neonatal case of skin blisters and erythema. While epidermolysis bullosa was initially suspected, immunofluorescence antigen mapping and genetic testing confirmed epidermolytic ichthyosis, with a heterozygous pathogenic variant in the KRT10 gene (c.467G>A, p.Arg156His). A mu...

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Main Authors: Elke Smits, Gunnar Naulaers, Maria C. Bolling, Eric Legius, Caroline Colmant
Format: Article
Language:English
Published: Wiley 2025-08-01
Series:Clinical Case Reports
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Online Access:https://doi.org/10.1002/ccr3.70682
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author Elke Smits
Gunnar Naulaers
Maria C. Bolling
Eric Legius
Caroline Colmant
author_facet Elke Smits
Gunnar Naulaers
Maria C. Bolling
Eric Legius
Caroline Colmant
author_sort Elke Smits
collection DOAJ
description ABSTRACT We present a neonatal case of skin blisters and erythema. While epidermolysis bullosa was initially suspected, immunofluorescence antigen mapping and genetic testing confirmed epidermolytic ichthyosis, with a heterozygous pathogenic variant in the KRT10 gene (c.467G>A, p.Arg156His). A multidisciplinary approach is essential for accurate diagnosis and treatment of neonatal blistering conditions.
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publishDate 2025-08-01
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series Clinical Case Reports
spelling doaj-art-1c196f7fef2c477b95c772d8c0e442d22025-08-22T07:33:07ZengWileyClinical Case Reports2050-09042025-08-01138n/an/a10.1002/ccr3.70682Neonatal Epidermolytic Ichthyosis Caused by a KRT10 Mutation (c.467G>A, p.Arg156His): A Case ReportElke Smits0Gunnar Naulaers1Maria C. Bolling2Eric Legius3Caroline Colmant4Department of Pediatrics University Hospitals Leuven Leuven BelgiumDepartment of Development and Regeneration KU Leuven Leuven BelgiumDepartment of Dermatology University Medical Center, University of Groningen Groningen the NetherlandsDepartment of Human Genetics KU Leuven and University Hospital Leuven Leuven BelgiumDepartment of Dermatology University Hospitals Leuven Leuven BelgiumABSTRACT We present a neonatal case of skin blisters and erythema. While epidermolysis bullosa was initially suspected, immunofluorescence antigen mapping and genetic testing confirmed epidermolytic ichthyosis, with a heterozygous pathogenic variant in the KRT10 gene (c.467G>A, p.Arg156His). A multidisciplinary approach is essential for accurate diagnosis and treatment of neonatal blistering conditions.https://doi.org/10.1002/ccr3.70682blistering skin diseasecongenital erythrodermaepidermolysis bullosaepidermolytic hyperkeratosisepidermolytic ichthyosis
spellingShingle Elke Smits
Gunnar Naulaers
Maria C. Bolling
Eric Legius
Caroline Colmant
Neonatal Epidermolytic Ichthyosis Caused by a KRT10 Mutation (c.467G>A, p.Arg156His): A Case Report
Clinical Case Reports
blistering skin disease
congenital erythroderma
epidermolysis bullosa
epidermolytic hyperkeratosis
epidermolytic ichthyosis
title Neonatal Epidermolytic Ichthyosis Caused by a KRT10 Mutation (c.467G>A, p.Arg156His): A Case Report
title_full Neonatal Epidermolytic Ichthyosis Caused by a KRT10 Mutation (c.467G>A, p.Arg156His): A Case Report
title_fullStr Neonatal Epidermolytic Ichthyosis Caused by a KRT10 Mutation (c.467G>A, p.Arg156His): A Case Report
title_full_unstemmed Neonatal Epidermolytic Ichthyosis Caused by a KRT10 Mutation (c.467G>A, p.Arg156His): A Case Report
title_short Neonatal Epidermolytic Ichthyosis Caused by a KRT10 Mutation (c.467G>A, p.Arg156His): A Case Report
title_sort neonatal epidermolytic ichthyosis caused by a krt10 mutation c 467g a p arg156his a case report
topic blistering skin disease
congenital erythroderma
epidermolysis bullosa
epidermolytic hyperkeratosis
epidermolytic ichthyosis
url https://doi.org/10.1002/ccr3.70682
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