Complete surgical correction of tetralogy of Fallot with Ebstein’s anomaly
Association of Ebstein’s anomaly of tricuspid valve (TV) with tetralogy of Fallot (TOF) is extremely rare. Their coexistence is unique as they modify each other’s physiology. We report a case of a girl child having this rare combination along with Diamond–Blackfan syndrome awaiting a bone marrow tra...
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| Format: | Article |
| Language: | English |
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Wolters Kluwer Medknow Publications
2024-11-01
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| Series: | Annals of Pediatric Cardiology |
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| Online Access: | https://journals.lww.com/10.4103/apc.apc_90_24 |
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| author | Zarin S. Rangwala Kaushik Ramachandran Sunil Sagar Subin Sukesan Baiju S. Dharan |
| author_facet | Zarin S. Rangwala Kaushik Ramachandran Sunil Sagar Subin Sukesan Baiju S. Dharan |
| author_sort | Zarin S. Rangwala |
| collection | DOAJ |
| description | Association of Ebstein’s anomaly of tricuspid valve (TV) with tetralogy of Fallot (TOF) is extremely rare. Their coexistence is unique as they modify each other’s physiology. We report a case of a girl child having this rare combination along with Diamond–Blackfan syndrome awaiting a bone marrow transplant. She underwent intracardiac repair for TOF along with cone reconstruction of the TV, as tricuspid regurgitation of Ebstein’s anomaly would worsen with TOF correction alone. Through this surgery, we aimed to achieve a competent pulmonary valve using a transannular patch with a monocusp and adequate relief of the right ventricular tract obstruction, thus preserving the right ventricular function, as both can affect the repaired TV function in the long term. The child had an uneventful postoperative course and is asymptomatic on follow-up. |
| format | Article |
| id | doaj-art-1a274bb851a848e0bb49bc294ed9d5a0 |
| institution | Kabale University |
| issn | 0974-2069 0974-5149 |
| language | English |
| publishDate | 2024-11-01 |
| publisher | Wolters Kluwer Medknow Publications |
| record_format | Article |
| series | Annals of Pediatric Cardiology |
| spelling | doaj-art-1a274bb851a848e0bb49bc294ed9d5a02024-12-06T05:55:00ZengWolters Kluwer Medknow PublicationsAnnals of Pediatric Cardiology0974-20690974-51492024-11-0117428528710.4103/apc.apc_90_24Complete surgical correction of tetralogy of Fallot with Ebstein’s anomalyZarin S. RangwalaKaushik RamachandranSunil SagarSubin SukesanBaiju S. DharanAssociation of Ebstein’s anomaly of tricuspid valve (TV) with tetralogy of Fallot (TOF) is extremely rare. Their coexistence is unique as they modify each other’s physiology. We report a case of a girl child having this rare combination along with Diamond–Blackfan syndrome awaiting a bone marrow transplant. She underwent intracardiac repair for TOF along with cone reconstruction of the TV, as tricuspid regurgitation of Ebstein’s anomaly would worsen with TOF correction alone. Through this surgery, we aimed to achieve a competent pulmonary valve using a transannular patch with a monocusp and adequate relief of the right ventricular tract obstruction, thus preserving the right ventricular function, as both can affect the repaired TV function in the long term. The child had an uneventful postoperative course and is asymptomatic on follow-up.https://journals.lww.com/10.4103/apc.apc_90_24cone repaircongenital heart diseasetricuspid valve |
| spellingShingle | Zarin S. Rangwala Kaushik Ramachandran Sunil Sagar Subin Sukesan Baiju S. Dharan Complete surgical correction of tetralogy of Fallot with Ebstein’s anomaly Annals of Pediatric Cardiology cone repair congenital heart disease tricuspid valve |
| title | Complete surgical correction of tetralogy of Fallot with Ebstein’s anomaly |
| title_full | Complete surgical correction of tetralogy of Fallot with Ebstein’s anomaly |
| title_fullStr | Complete surgical correction of tetralogy of Fallot with Ebstein’s anomaly |
| title_full_unstemmed | Complete surgical correction of tetralogy of Fallot with Ebstein’s anomaly |
| title_short | Complete surgical correction of tetralogy of Fallot with Ebstein’s anomaly |
| title_sort | complete surgical correction of tetralogy of fallot with ebstein s anomaly |
| topic | cone repair congenital heart disease tricuspid valve |
| url | https://journals.lww.com/10.4103/apc.apc_90_24 |
| work_keys_str_mv | AT zarinsrangwala completesurgicalcorrectionoftetralogyoffallotwithebsteinsanomaly AT kaushikramachandran completesurgicalcorrectionoftetralogyoffallotwithebsteinsanomaly AT sunilsagar completesurgicalcorrectionoftetralogyoffallotwithebsteinsanomaly AT subinsukesan completesurgicalcorrectionoftetralogyoffallotwithebsteinsanomaly AT baijusdharan completesurgicalcorrectionoftetralogyoffallotwithebsteinsanomaly |