Echocardiographic screening for the anomalous aortic origin of coronary arteries

Aims We sought to determine the diagnostic performance, clinical profiles and outcomes of anomalous aortic origin of coronary arteries (AAOCA) using a standardised echocardiographic approach in young adults and athletes.Methods In 2015–2019, we screened 5998 outpatients (age 16 years (Q1–Q3: 11, 36)...

Full description

Saved in:
Bibliographic Details
Main Authors: Francesco Bianco, Valentina Bucciarelli, Sabina Gallina, Massimo Colaneri, Francesca Chiara Surace, Federica Valentina Iezzi, Martina Primavera, Annaclara Biasi, Giuliano Giusti, Emanuela Berton, Monica Baldoni, Giulia Renda, Alessandra Baldinelli, Marco Pozzi
Format: Article
Language:English
Published: BMJ Publishing Group 2021-02-01
Series:Open Heart
Online Access:https://openheart.bmj.com/content/8/1/e001495.full
Tags: Add Tag
No Tags, Be the first to tag this record!
_version_ 1846169978052542464
author Francesco Bianco
Valentina Bucciarelli
Sabina Gallina
Massimo Colaneri
Francesca Chiara Surace
Federica Valentina Iezzi
Martina Primavera
Annaclara Biasi
Giuliano Giusti
Emanuela Berton
Monica Baldoni
Giulia Renda
Alessandra Baldinelli
Marco Pozzi
author_facet Francesco Bianco
Valentina Bucciarelli
Sabina Gallina
Massimo Colaneri
Francesca Chiara Surace
Federica Valentina Iezzi
Martina Primavera
Annaclara Biasi
Giuliano Giusti
Emanuela Berton
Monica Baldoni
Giulia Renda
Alessandra Baldinelli
Marco Pozzi
author_sort Francesco Bianco
collection DOAJ
description Aims We sought to determine the diagnostic performance, clinical profiles and outcomes of anomalous aortic origin of coronary arteries (AAOCA) using a standardised echocardiographic approach in young adults and athletes.Methods In 2015–2019, we screened 5998 outpatients (age 16 years (Q1–Q3: 11, 36)), referred for routine echocardiography, using four specific echocardiographic windows: parasternal short/long axis and apical 4/5-chambers view. Coronary CT confirmed AAOCA. For the performance analysis, 300 coronary-CT scans were available; two independent and double-blinded physicians retrospectively reviewed echocardiographic images.Results A total of 47 AAOCA was diagnosed; the overall prevalence was 0.0078%. Over 5 years, we found a significant increment of AAOCA diagnostic rate (P for trend=0.002). Syncope (n=17/47) and palpitations (n=6/47) were prevalent symptoms. All patients suspended sports activity at the diagnosis. Twenty-seven patients underwent surgery, while 20 underwent a conservative medical treatment. All patients are alive at a median follow-up of 3±1.6 years; only surgical repairs restarted their activity. Our method showed better sensitivity than traditional short-axis evaluation: 93% vs 83%, p=0.0030 (AUC 0.96 (95% CI 0.92, 0.99) and AUC 0.89 (95% CI 0.83, 0.95), respectively), with a good interobserver agreement (95%, k=0.83, p<0.001).Conclusions The application of a standardised echocardiographic approach for AAOCA detection led to a significantly increased rate of identified anomalies. This approach demonstrated higher sensitivity than the traditional echocardiographic assessment. Implementing this protocol in clinical practice may help improve the AAOCA diagnosis in young adults and athletes.Trial registration number NCT04224090.
format Article
id doaj-art-109058a9f98d451cb09f7833e8934ca2
institution Kabale University
issn 2053-3624
language English
publishDate 2021-02-01
publisher BMJ Publishing Group
record_format Article
series Open Heart
spelling doaj-art-109058a9f98d451cb09f7833e8934ca22024-11-12T05:50:07ZengBMJ Publishing GroupOpen Heart2053-36242021-02-018110.1136/openhrt-2020-001495Echocardiographic screening for the anomalous aortic origin of coronary arteriesFrancesco Bianco0Valentina Bucciarelli1Sabina Gallina2Massimo Colaneri3Francesca Chiara Surace4Federica Valentina Iezzi5Martina Primavera6Annaclara Biasi7Giuliano Giusti8Emanuela Berton9Monica Baldoni10Giulia Renda11Alessandra Baldinelli12Marco Pozzi13Pediatric and Congenital Cardiology and Cardiac Surgery, Azienda Ospedaliero Universitaria Ospedali Riuniti di Ancona Umberto I G M Lancisi G Salesi, Ancona, Marche, ItalyDepartment of Neuroscience, Imaging and Clinical Sciences, Universita degli Studi Gabriele d`Annunzio Chieti e Pescara, Chieti, Abruzzo, ItalyDepartment of Neuroscience, Imaging and Clinical Sciences, Universita degli Studi Gabriele d`Annunzio Chieti e Pescara, Chieti, Abruzzo, ItalyPediatric and Congenital Cardiology and Cardiac Surgery, Azienda Ospedaliero Universitaria Ospedali Riuniti di Ancona Umberto I G M Lancisi G Salesi, Ancona, Marche, ItalyPediatric and Congenital Cardiology and Cardiac Surgery, Azienda Ospedaliero Universitaria Ospedali Riuniti di Ancona Umberto I G M Lancisi G Salesi, Ancona, Marche, ItalyPediatric and Congenital Cardiology and Cardiac Surgery, Azienda Ospedaliero Universitaria Ospedali Riuniti di Ancona Umberto I G M Lancisi G Salesi, Ancona, Marche, ItalyDepartment of Neuroscience, Imaging and Clinical Sciences, Universita degli Studi Gabriele d`Annunzio Chieti e Pescara, Chieti, Abruzzo, ItalyDepartment of Neuroscience, Imaging and Clinical Sciences, Universita degli Studi Gabriele d`Annunzio Chieti e Pescara, Chieti, Abruzzo, ItalyPediatric and Congenital Cardiology and Cardiac Surgery, Azienda Ospedaliero Universitaria Ospedali Riuniti di Ancona Umberto I G M Lancisi G Salesi, Ancona, Marche, ItalyPediatric and Congenital Cardiology and Cardiac Surgery, Azienda Ospedaliero Universitaria Ospedali Riuniti di Ancona Umberto I G M Lancisi G Salesi, Ancona, Marche, ItalyPediatric and Congenital Cardiology and Cardiac Surgery, Azienda Ospedaliero Universitaria Ospedali Riuniti di Ancona Umberto I G M Lancisi G Salesi, Ancona, Marche, ItalyDepartment of Neuroscience, Imaging and Clinical Sciences, Universita degli Studi Gabriele d`Annunzio Chieti e Pescara, Chieti, Abruzzo, ItalyPediatric and Congenital Cardiology and Cardiac Surgery, Azienda Ospedaliero Universitaria Ospedali Riuniti di Ancona Umberto I G M Lancisi G Salesi, Ancona, Marche, ItalyPediatric and Congenital Cardiology and Cardiac Surgery, Azienda Ospedaliero Universitaria Ospedali Riuniti di Ancona Umberto I G M Lancisi G Salesi, Ancona, Marche, ItalyAims We sought to determine the diagnostic performance, clinical profiles and outcomes of anomalous aortic origin of coronary arteries (AAOCA) using a standardised echocardiographic approach in young adults and athletes.Methods In 2015–2019, we screened 5998 outpatients (age 16 years (Q1–Q3: 11, 36)), referred for routine echocardiography, using four specific echocardiographic windows: parasternal short/long axis and apical 4/5-chambers view. Coronary CT confirmed AAOCA. For the performance analysis, 300 coronary-CT scans were available; two independent and double-blinded physicians retrospectively reviewed echocardiographic images.Results A total of 47 AAOCA was diagnosed; the overall prevalence was 0.0078%. Over 5 years, we found a significant increment of AAOCA diagnostic rate (P for trend=0.002). Syncope (n=17/47) and palpitations (n=6/47) were prevalent symptoms. All patients suspended sports activity at the diagnosis. Twenty-seven patients underwent surgery, while 20 underwent a conservative medical treatment. All patients are alive at a median follow-up of 3±1.6 years; only surgical repairs restarted their activity. Our method showed better sensitivity than traditional short-axis evaluation: 93% vs 83%, p=0.0030 (AUC 0.96 (95% CI 0.92, 0.99) and AUC 0.89 (95% CI 0.83, 0.95), respectively), with a good interobserver agreement (95%, k=0.83, p<0.001).Conclusions The application of a standardised echocardiographic approach for AAOCA detection led to a significantly increased rate of identified anomalies. This approach demonstrated higher sensitivity than the traditional echocardiographic assessment. Implementing this protocol in clinical practice may help improve the AAOCA diagnosis in young adults and athletes.Trial registration number NCT04224090.https://openheart.bmj.com/content/8/1/e001495.full
spellingShingle Francesco Bianco
Valentina Bucciarelli
Sabina Gallina
Massimo Colaneri
Francesca Chiara Surace
Federica Valentina Iezzi
Martina Primavera
Annaclara Biasi
Giuliano Giusti
Emanuela Berton
Monica Baldoni
Giulia Renda
Alessandra Baldinelli
Marco Pozzi
Echocardiographic screening for the anomalous aortic origin of coronary arteries
Open Heart
title Echocardiographic screening for the anomalous aortic origin of coronary arteries
title_full Echocardiographic screening for the anomalous aortic origin of coronary arteries
title_fullStr Echocardiographic screening for the anomalous aortic origin of coronary arteries
title_full_unstemmed Echocardiographic screening for the anomalous aortic origin of coronary arteries
title_short Echocardiographic screening for the anomalous aortic origin of coronary arteries
title_sort echocardiographic screening for the anomalous aortic origin of coronary arteries
url https://openheart.bmj.com/content/8/1/e001495.full
work_keys_str_mv AT francescobianco echocardiographicscreeningfortheanomalousaorticoriginofcoronaryarteries
AT valentinabucciarelli echocardiographicscreeningfortheanomalousaorticoriginofcoronaryarteries
AT sabinagallina echocardiographicscreeningfortheanomalousaorticoriginofcoronaryarteries
AT massimocolaneri echocardiographicscreeningfortheanomalousaorticoriginofcoronaryarteries
AT francescachiarasurace echocardiographicscreeningfortheanomalousaorticoriginofcoronaryarteries
AT federicavalentinaiezzi echocardiographicscreeningfortheanomalousaorticoriginofcoronaryarteries
AT martinaprimavera echocardiographicscreeningfortheanomalousaorticoriginofcoronaryarteries
AT annaclarabiasi echocardiographicscreeningfortheanomalousaorticoriginofcoronaryarteries
AT giulianogiusti echocardiographicscreeningfortheanomalousaorticoriginofcoronaryarteries
AT emanuelaberton echocardiographicscreeningfortheanomalousaorticoriginofcoronaryarteries
AT monicabaldoni echocardiographicscreeningfortheanomalousaorticoriginofcoronaryarteries
AT giuliarenda echocardiographicscreeningfortheanomalousaorticoriginofcoronaryarteries
AT alessandrabaldinelli echocardiographicscreeningfortheanomalousaorticoriginofcoronaryarteries
AT marcopozzi echocardiographicscreeningfortheanomalousaorticoriginofcoronaryarteries