PRİMARY CONJUNCTIVAL LYMPHOMA, 2 CASES

Introduction: Extranodal marginal zone lymphoma (EMZL) is the most common subtype of conjunctival lymphoma. Management of conjunctival lymphoma consists of radiotherapy, surgery, chemotherapy, antibiotics and targeted therapies (Anti-CD 20) based on case series and retrospective studies. Appropriate...

Full description

Saved in:
Bibliographic Details
Main Authors: Günay Süleymanlı, Yasemin Aydınalp Camadan, Tuğba Toyran, Berksoy Şahin
Format: Article
Language:English
Published: Elsevier 2024-12-01
Series:Hematology, Transfusion and Cell Therapy
Online Access:http://www.sciencedirect.com/science/article/pii/S2531137924029092
Tags: Add Tag
No Tags, Be the first to tag this record!
_version_ 1846107609907593216
author Günay Süleymanlı
Yasemin Aydınalp Camadan
Tuğba Toyran
Berksoy Şahin
author_facet Günay Süleymanlı
Yasemin Aydınalp Camadan
Tuğba Toyran
Berksoy Şahin
author_sort Günay Süleymanlı
collection DOAJ
description Introduction: Extranodal marginal zone lymphoma (EMZL) is the most common subtype of conjunctival lymphoma. Management of conjunctival lymphoma consists of radiotherapy, surgery, chemotherapy, antibiotics and targeted therapies (Anti-CD 20) based on case series and retrospective studies. Appropriate treatment should be chosen based on the type of lymphoma, extent of spread, and patient-specific factors. We present two patients with localized disease diagnosed with primary conjunctival EZML by biopsy, for whom we planned different treatment plans. Case Reports: Case 1: A 64-year-old female patient presented with a pink-red mass on the lateral conjunctiva of her right eye. (Fig. 1A) Conjunctival biopsy was reported as Non-Hodgkin lymphoma, EMZL.(CD 20(+) and Ki-67 3-4%) No extraocular involvement on PET/CT. Orbital MRI showed a 2.5 cm soft tissue lesion surrounding the right globe laterally and posteriorly. The patient started rituximab and bendamustine treatment, and the lesion in the right orbit was not observed in the current follow-up imaging after 3 cycles of treatment. (Fig. 1B) The patient continued with rituximab and bendamustine treatment.Case 2: When the 52-year-old female patient first appeared two years ago, a conjunctival biopsy revealed that she had EMZL. Radiotherapy was recommended for her localized disease, but she declined it. She received eight cycles of rituximab treatment and was monitored in remission. One year later, salmon-colored lesions were found in the inner corner of both eyes. EZML was also found in the new biopsy. There was no ocular involvement. The patient received 6 cycles of rituximab bendamustine and maintenance rituximab for recurrent and bilateral lesions. We are currently monitoring the patient and the disease is in complete remission. Discussion: Lymphoma is one of the most frequently occurring malignant tumors of the conjunctiva. In patients with lesions that like a ''salmon patch'' and unexplained chronic follicular conjunctivitis, lymphoma should be suspected.
format Article
id doaj-art-0b6c8581c9804a92b7a7e686b37703a6
institution Kabale University
issn 2531-1379
language English
publishDate 2024-12-01
publisher Elsevier
record_format Article
series Hematology, Transfusion and Cell Therapy
spelling doaj-art-0b6c8581c9804a92b7a7e686b37703a62024-12-26T08:57:09ZengElsevierHematology, Transfusion and Cell Therapy2531-13792024-12-0146S69S70PRİMARY CONJUNCTIVAL LYMPHOMA, 2 CASESGünay Süleymanlı0Yasemin Aydınalp Camadan1Tuğba Toyran2Berksoy Şahin3Cukurova University, Faculty of Medicine, Department of Internal Medicine; Corresponding author.Cukurova University, Faculty of Medicine, Department of Medical OncologyCukurova University, Faculty of Medicine, Department of PathologyCukurova University, Faculty of Medicine, Department of Medical OncologyIntroduction: Extranodal marginal zone lymphoma (EMZL) is the most common subtype of conjunctival lymphoma. Management of conjunctival lymphoma consists of radiotherapy, surgery, chemotherapy, antibiotics and targeted therapies (Anti-CD 20) based on case series and retrospective studies. Appropriate treatment should be chosen based on the type of lymphoma, extent of spread, and patient-specific factors. We present two patients with localized disease diagnosed with primary conjunctival EZML by biopsy, for whom we planned different treatment plans. Case Reports: Case 1: A 64-year-old female patient presented with a pink-red mass on the lateral conjunctiva of her right eye. (Fig. 1A) Conjunctival biopsy was reported as Non-Hodgkin lymphoma, EMZL.(CD 20(+) and Ki-67 3-4%) No extraocular involvement on PET/CT. Orbital MRI showed a 2.5 cm soft tissue lesion surrounding the right globe laterally and posteriorly. The patient started rituximab and bendamustine treatment, and the lesion in the right orbit was not observed in the current follow-up imaging after 3 cycles of treatment. (Fig. 1B) The patient continued with rituximab and bendamustine treatment.Case 2: When the 52-year-old female patient first appeared two years ago, a conjunctival biopsy revealed that she had EMZL. Radiotherapy was recommended for her localized disease, but she declined it. She received eight cycles of rituximab treatment and was monitored in remission. One year later, salmon-colored lesions were found in the inner corner of both eyes. EZML was also found in the new biopsy. There was no ocular involvement. The patient received 6 cycles of rituximab bendamustine and maintenance rituximab for recurrent and bilateral lesions. We are currently monitoring the patient and the disease is in complete remission. Discussion: Lymphoma is one of the most frequently occurring malignant tumors of the conjunctiva. In patients with lesions that like a ''salmon patch'' and unexplained chronic follicular conjunctivitis, lymphoma should be suspected.http://www.sciencedirect.com/science/article/pii/S2531137924029092
spellingShingle Günay Süleymanlı
Yasemin Aydınalp Camadan
Tuğba Toyran
Berksoy Şahin
PRİMARY CONJUNCTIVAL LYMPHOMA, 2 CASES
Hematology, Transfusion and Cell Therapy
title PRİMARY CONJUNCTIVAL LYMPHOMA, 2 CASES
title_full PRİMARY CONJUNCTIVAL LYMPHOMA, 2 CASES
title_fullStr PRİMARY CONJUNCTIVAL LYMPHOMA, 2 CASES
title_full_unstemmed PRİMARY CONJUNCTIVAL LYMPHOMA, 2 CASES
title_short PRİMARY CONJUNCTIVAL LYMPHOMA, 2 CASES
title_sort primary conjunctival lymphoma 2 cases
url http://www.sciencedirect.com/science/article/pii/S2531137924029092
work_keys_str_mv AT gunaysuleymanlı primaryconjunctivallymphoma2cases
AT yaseminaydınalpcamadan primaryconjunctivallymphoma2cases
AT tugbatoyran primaryconjunctivallymphoma2cases
AT berksoysahin primaryconjunctivallymphoma2cases