Carcinoma hepatocelular após cirugía de Fontan: relato de caso
BACKGROUND: Single ventricle includes various cardiac abnormalities in which either one ventricle is underdeveloped or a ventricular septal wall did not form, leading to the mixing of arterial and venous blood in the heart. The Fontan procedure separates the systemic and pulmonary circulations becau...
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Sociedade Galega de Medicina Interna
2025-04-01
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| Series: | Galicia Clínica |
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| Online Access: | https://ojs.galiciaclinica.info/gc/article/view/1431 |
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| author | Joana Ribeiro Lara Adelino |
| author_facet | Joana Ribeiro Lara Adelino |
| author_sort | Joana Ribeiro |
| collection | DOAJ |
| description | BACKGROUND: Single ventricle includes various cardiac abnormalities in which either one ventricle is underdeveloped or a ventricular septal wall did not form, leading to the mixing of arterial and venous blood in the heart. The Fontan procedure separates the systemic and pulmonary circulations because a surgical cavopulmonary connection is made. After this procedure, there is an increased systemic venous pressure, leading to low hepatic perfusion pressure and oxygenation, fibrosis, cirrhosis and ultimately hepatocellular carcinoma.
PATIENT AND METHODS: This case report details a 40-year-old man who received the Fontan procedure, developing symptoms similar to cardiac failure 30 years later. After further evaluation, findings were consistent with hepatocellular carcinoma with lung metastasis, leading to death in less than one month.
RESULTS AND CONCLUSION: Fontan patients must be screened for associated liver disease with cirrhosis and hepatocellular carcinoma to prevent disease progression and its detection in advanced stages. Despite the regular follow-up in a Cardiology consultation, we point out the importance of a multidisciplinary approach to screening for complications of the Fontan procedure. |
| format | Article |
| id | doaj-art-0750bcd32ccf45bfbc816b2bc3e254e7 |
| institution | DOAJ |
| issn | 0304-4866 1989-3922 |
| language | English |
| publishDate | 2025-04-01 |
| publisher | Sociedade Galega de Medicina Interna |
| record_format | Article |
| series | Galicia Clínica |
| spelling | doaj-art-0750bcd32ccf45bfbc816b2bc3e254e72025-08-20T03:09:07ZengSociedade Galega de Medicina InternaGalicia Clínica0304-48661989-39222025-04-01854262810.22546/75/41711431Carcinoma hepatocelular após cirugía de Fontan: relato de casoJoana Ribeiro0https://orcid.org/0000-0003-1821-8334Lara Adelino1Centro Hospitalar do Médio TejoCentro Hospitalar do Médio TejoBACKGROUND: Single ventricle includes various cardiac abnormalities in which either one ventricle is underdeveloped or a ventricular septal wall did not form, leading to the mixing of arterial and venous blood in the heart. The Fontan procedure separates the systemic and pulmonary circulations because a surgical cavopulmonary connection is made. After this procedure, there is an increased systemic venous pressure, leading to low hepatic perfusion pressure and oxygenation, fibrosis, cirrhosis and ultimately hepatocellular carcinoma. PATIENT AND METHODS: This case report details a 40-year-old man who received the Fontan procedure, developing symptoms similar to cardiac failure 30 years later. After further evaluation, findings were consistent with hepatocellular carcinoma with lung metastasis, leading to death in less than one month. RESULTS AND CONCLUSION: Fontan patients must be screened for associated liver disease with cirrhosis and hepatocellular carcinoma to prevent disease progression and its detection in advanced stages. Despite the regular follow-up in a Cardiology consultation, we point out the importance of a multidisciplinary approach to screening for complications of the Fontan procedure.https://ojs.galiciaclinica.info/gc/article/view/1431carcinoma hepatocelularcirugía de fontancirrosiscuidados paliativos |
| spellingShingle | Joana Ribeiro Lara Adelino Carcinoma hepatocelular após cirugía de Fontan: relato de caso Galicia Clínica carcinoma hepatocelular cirugía de fontan cirrosis cuidados paliativos |
| title | Carcinoma hepatocelular após cirugía de Fontan: relato de caso |
| title_full | Carcinoma hepatocelular após cirugía de Fontan: relato de caso |
| title_fullStr | Carcinoma hepatocelular após cirugía de Fontan: relato de caso |
| title_full_unstemmed | Carcinoma hepatocelular após cirugía de Fontan: relato de caso |
| title_short | Carcinoma hepatocelular após cirugía de Fontan: relato de caso |
| title_sort | carcinoma hepatocelular apos cirugia de fontan relato de caso |
| topic | carcinoma hepatocelular cirugía de fontan cirrosis cuidados paliativos |
| url | https://ojs.galiciaclinica.info/gc/article/view/1431 |
| work_keys_str_mv | AT joanaribeiro carcinomahepatocelularaposcirugiadefontanrelatodecaso AT laraadelino carcinomahepatocelularaposcirugiadefontanrelatodecaso |