Hairy B-cell lymphoproliferative disorder and its differential diagnosis: a case with long-term follow-up

Hairy B-cell lymphoproliferative disorder (HBLD) is one of chronic polyclonal B-cell lymphocytosis. We report a 47-year-old female Japanese patient diagnosed as having HBLD based on lymphocytosis with hairy cell appearance and characteristic phenotypes including CD11c+, and without B-cell monoclonal...

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Main Authors: Kensuke Matsuda, Yosuke Matsumoto, Mihiko Yoshida, Kazuho Shimura, Hiroto Kaneko, Tohru Inaba, Shigeo Horiike, Junya Kuroda, Masafumi Taniwaki
Format: Article
Language:English
Published: PAGEPress Publications 2017-09-01
Series:Mediterranean Journal of Hematology and Infectious Diseases
Online Access:http://www.mjhid.org/index.php/mjhid/article/view/3056
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author Kensuke Matsuda
Yosuke Matsumoto
Mihiko Yoshida
Kazuho Shimura
Hiroto Kaneko
Tohru Inaba
Shigeo Horiike
Junya Kuroda
Masafumi Taniwaki
author_facet Kensuke Matsuda
Yosuke Matsumoto
Mihiko Yoshida
Kazuho Shimura
Hiroto Kaneko
Tohru Inaba
Shigeo Horiike
Junya Kuroda
Masafumi Taniwaki
author_sort Kensuke Matsuda
collection DOAJ
description Hairy B-cell lymphoproliferative disorder (HBLD) is one of chronic polyclonal B-cell lymphocytosis. We report a 47-year-old female Japanese patient diagnosed as having HBLD based on lymphocytosis with hairy cell appearance and characteristic phenotypes including CD11c+, and without B-cell monoclonalities. She was a non-smoker, and possessed HLA-DR4. She has been closely followed up without treatment and lymphoma development for over five years. Although this disease is quite rare and has been reported, to our knowledge, in only 13 Japanese cases, an accurate diagnosis, particularly differential diagnosis from persistent polyclonal B-cell lymphocytosis or hairy cell leukemia-Japanese variant is essential for the prevention of unnecessary treatments.
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institution Kabale University
issn 2035-3006
language English
publishDate 2017-09-01
publisher PAGEPress Publications
record_format Article
series Mediterranean Journal of Hematology and Infectious Diseases
spelling doaj-art-0231e8b933714b3e86d0d241313344632025-01-02T08:47:01ZengPAGEPress PublicationsMediterranean Journal of Hematology and Infectious Diseases2035-30062017-09-0191e2017054e201705410.4084/mjhid.2017.0541708Hairy B-cell lymphoproliferative disorder and its differential diagnosis: a case with long-term follow-upKensuke MatsudaYosuke MatsumotoMihiko YoshidaKazuho ShimuraHiroto KanekoTohru InabaShigeo HoriikeJunya KurodaMasafumi TaniwakiHairy B-cell lymphoproliferative disorder (HBLD) is one of chronic polyclonal B-cell lymphocytosis. We report a 47-year-old female Japanese patient diagnosed as having HBLD based on lymphocytosis with hairy cell appearance and characteristic phenotypes including CD11c+, and without B-cell monoclonalities. She was a non-smoker, and possessed HLA-DR4. She has been closely followed up without treatment and lymphoma development for over five years. Although this disease is quite rare and has been reported, to our knowledge, in only 13 Japanese cases, an accurate diagnosis, particularly differential diagnosis from persistent polyclonal B-cell lymphocytosis or hairy cell leukemia-Japanese variant is essential for the prevention of unnecessary treatments.http://www.mjhid.org/index.php/mjhid/article/view/3056
spellingShingle Kensuke Matsuda
Yosuke Matsumoto
Mihiko Yoshida
Kazuho Shimura
Hiroto Kaneko
Tohru Inaba
Shigeo Horiike
Junya Kuroda
Masafumi Taniwaki
Hairy B-cell lymphoproliferative disorder and its differential diagnosis: a case with long-term follow-up
Mediterranean Journal of Hematology and Infectious Diseases
title Hairy B-cell lymphoproliferative disorder and its differential diagnosis: a case with long-term follow-up
title_full Hairy B-cell lymphoproliferative disorder and its differential diagnosis: a case with long-term follow-up
title_fullStr Hairy B-cell lymphoproliferative disorder and its differential diagnosis: a case with long-term follow-up
title_full_unstemmed Hairy B-cell lymphoproliferative disorder and its differential diagnosis: a case with long-term follow-up
title_short Hairy B-cell lymphoproliferative disorder and its differential diagnosis: a case with long-term follow-up
title_sort hairy b cell lymphoproliferative disorder and its differential diagnosis a case with long term follow up
url http://www.mjhid.org/index.php/mjhid/article/view/3056
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